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Long-term management of patients with hypoplastic left heart syndrome: the diagnostic approach at All Children's Hospital

Published online by Cambridge University Press:  13 December 2011

Gul H. Dadlani ,
Katherine Braley ,
Elimarys Perez-Colon ,
Gary Stapleton ,
Marguerite Crawford ,
Dima Turpin ,
Ivan Wilmot ,
Grace Freire ,
Jamie Decker  and
Richard Martinez
Gul H. Dadlani*
Affiliation:
Division of Pediatric Cardiology, All Children's Hospital Heart Institute, Saint Petersburg, Florida, United States of America Department of Pediatrics, University of South Florida, Saint Petersburg and Tampa, Florida, United States of America
Katherine Braley
Affiliation:
Department of Pediatrics, University of South Florida, Saint Petersburg and Tampa, Florida, United States of America
Elimarys Perez-Colon
Affiliation:
Department of Pediatrics, University of South Florida, Saint Petersburg and Tampa, Florida, United States of America
Gary Stapleton
Affiliation:
Division of Pediatric Cardiology, All Children's Hospital Heart Institute, Saint Petersburg, Florida, United States of America
Marguerite Crawford
Affiliation:
Division of Pediatric Cardiology, All Children's Hospital Heart Institute, Saint Petersburg, Florida, United States of America
Dima Turpin
Affiliation:
Division of Pediatric Cardiology, All Children's Hospital Heart Institute, Saint Petersburg, Florida, United States of America
Ivan Wilmot
Affiliation:
Division of Pediatric Cardiology, All Children's Hospital Heart Institute, Saint Petersburg, Florida, United States of America
Grace Freire
Affiliation:
Division of Pediatric Cardiology, All Children's Hospital Heart Institute, Saint Petersburg, Florida, United States of America
Jamie Decker
Affiliation:
Division of Pediatric Cardiology, All Children's Hospital Heart Institute, Saint Petersburg, Florida, United States of America
Richard Martinez
Affiliation:
Department of Pediatrics, University of South Florida, Saint Petersburg and Tampa, Florida, United States of America Division of Pediatric Cardiology, The Congenital Heart Institute of Florida (CHIF), Pediatric Cardiology Associates/Pediatrix Medical Group, All Children's Hospital, Saint Petersburg, Florida, United States of America
*
Correspondence to: Dr G. H. Dadlani, MD, All Children's Heart Institute, 2nd Floor Outpatient Care Center, 601, 5th Street South, Saint Petersburg, Florida 33701, United States of America. Tel: 727-767-3333; Fax: 727-767-8990; E-mail: [email protected]
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Abstract

Improved survival in children with hypoplastic left heart syndrome has created a sub-population of children and young adults who are living with functionally univentricular physiology. Routine surveillance with comprehensive screening for structural cardiac disease, functional cardiac disease, arrhythmias, thromboembolic disease, and associated dysfunction of end organs is important. Future directives will better define the plans of care for routine surveillance in patients with hypoplastic left heart syndrome.

Keywords

Fontansingle ventriclefunctionally univentricular hearthypoplastic left heart syndromefollow-upadult congenital cardiac diseaseNorwood operation
Type
Original Article
Information
Cardiology in the Young , Volume 21 , Issue S2: A Holistic Approach to Hypoplastic Left Heart Syndrome and other evolving challenges in Pediatric and Congenital Cardiac Disease , 13 December 2011 , pp. 80 - 87
Copyright
Copyright © Cambridge University Press 2011

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