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Life-long follow-up in congenitally corrected transposition

Published online by Cambridge University Press:  01 November 2007

Wei-Jen Shih ,
Jacqueline A. Noonan  and
Alberto Mazzoleni
Wei-Jen Shih*
Affiliation:
Nuclear Medicine Service, Lexington Veterans Administration Medical Center, Lexington, Kentucky, United States of America Department of Diagnostic Radiology, College of Medicine, University of Kentucky, Lexington, Kentucky, United States of America
Jacqueline A. Noonan
Affiliation:
Department of Pediatrics, College of Medicine, University of Kentucky, Lexington, Kentucky, United States of America
Alberto Mazzoleni
Affiliation:
Cardiovascular Section, Medicine Service, United States of America Division of Cardiovascular Medicine, Department of Internal Medicine, College of Medicine, University of Kentucky, Lexington, Kentucky, United States of America
*
Correspondence to: Dr Wei-Jen Shih, Nuclear Medicine Service, Lexington VA Medical Center, 1101 Veterans Drive, Lexington, KY 40502, USA. Tel: +1 859 381 5928; Fax: +1 850 381 5934; E-mail: [email protected]
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Abstract

A male patient with congenitally corrected transposition, with no associated cardiac malformations, was diagnosed in childhood and followed until his death at age 28. He underwent two cardiac gated single photon emission computed tomographies over a two year period, which demonstrated progression of ischaemia and reduction of systolic function. The findings suggest that, when the systemic ventricle is perfused by the morphologically right coronary artery, there may be inadequate perfusion to supply any subsequent extensive hypertrophy.

Keywords

Congenital heart diseasedual isotope cardiac single photon emission computed tomographic studymyocardial perfusionleft ventricle ejection fractioncoronary angiography
Type
Brief Report
Information
Cardiology in the Young , Volume 17 , Issue 6 , December 2007 , pp. 681 - 684
Copyright
Copyright © Cambridge University Press 2007

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