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Left ventricular outflow tract obstruction in a patient with pulmonary atresia with intact ventricle septum following Fontan procedure: a rare complication

Published online by Cambridge University Press:  14 May 2021

Daiji Takajo*
Affiliation:
Department of Pediatrics, Children’s Hospital of Michigan, Detroit, MI, USA
Preetha L. Balakrishnan
Affiliation:
Division of Pediatric Cardiology, Department of Pediatrics, Children’s Hospital of Michigan, Wayne State University, Detroit, MI, USA
Sanjeev Aggarwal
Affiliation:
Division of Pediatric Cardiology, Department of Pediatrics, Children’s Hospital of Michigan, Wayne State University, Detroit, MI, USA
*
Author for correspondence: D. Takajo, Department of Pediatrics, Children’s Hospital of Michigan, 3901 Beaubien Boulevard, Detroit, MI, 48201, USA. Tel: +745 1892; Fax: +993 7118. E-mail: [email protected]

Abstract

Left ventricular outflow tract obstruction in patients with pulmonary atresia with intact ventricular septum has been rarely reported. Data are lacking on the impact and management of systemic ventricular outflow tract obstruction that developed following the Fontan procedure. We report a case of an 8-year-old male who developed left ventricular outflow tract obstruction 6 months after the Fontan procedure.

Type
Brief Report
Copyright
© The Author(s), 2021. Published by Cambridge University Press

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References

Franken, LC, Admiraal, M, Verrall, CE et al. Improved long-term outcomes in double-inlet left ventricle and tricuspid atresia with transposed great arteries: systemic outflow tract obstruction present at birth defines long-term outcome. Eur J Cardiothorac Surg 2017; 51: 10511057.CrossRefGoogle ScholarPubMed
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