Hostname: page-component-78c5997874-8bhkd Total loading time: 0 Render date: 2024-11-19T04:24:23.267Z Has data issue: false hasContentIssue false
  • English
  • Français

Left aortic arch with right descending aorta and severe coarctation: an unusual “vascular clamp” with airway compression

Part of: Ventricular Septal Defect (VSD) Cardiac Morphology

Published online by Cambridge University Press:  13 June 2018

Ronak Sheth ,
Roy Varghese  and
Kothandam Sivakumar
Ronak Sheth
Affiliation:
Department of Pediatric Cardiology, Madras Medical Mission, Chennai, India
Roy Varghese
Affiliation:
Department of Pediatric Cardiology, Madras Medical Mission, Chennai, India
Kothandam Sivakumar*
Affiliation:
Department of Pediatric Cardiology, Madras Medical Mission, Chennai, India
*
Author for correspondence: Dr K. Sivakumar, MD, DM, Head of Department of Pediatric Cardiology, Institute of Cardiovascular Diseases, Madras Medical Mission, 4A, Dr J J Nagar, Mogappair, Chennai 600089, India. Tel: +91 9444449966; Fax: +91 44 26565859; E-mail: [email protected]
Get access Rights & Permissions [Opens in a new window]

Abstract

Left aortic arch with right descending aorta is a rare congenital anomaly. We describe the clinical presentation of this unusual anomaly associated with cardiorespiratory compromise from severe aortic obstruction and left main bronchus compression. The anatomical peculiarities, embryological basis, and surgical solutions are presented.

Keywords

Aortic archcircumflex aortaembryology of aortic archaortic translocationcoarctation
Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 8 , August 2018 , pp. 1056 - 1058
Check for updates
Copyright
© Cambridge University Press 2018 

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

Footnotes

Cite this article: Sheth R, Varghese R, Sivakumar K. (2018) Left aortic arch with right descending aorta and severe coarctation: an unusual “vascular clamp” with airway compression. Cardiology in the Young28: 1056–1058. doi: 10.1017/S1047951118000665

References

1. Ergin, MA, Jayaram, N, LaCorte, M. Left aortic arch and right descending aorta: diagnostic and therapeutic implications of a rare type of vascular ring. Ann Thorac Surg 1981; 31: 82–85.Google Scholar
2. Dominiguez, R, Sang-Oh, K, Dorst, JP. Left aortic arch with right descending aorta. Am J Roentgenol 1978; 130: 917–920.Google Scholar
3. Singh, GK, Greenberg, SB, Balsara, RK. Diagnostic dilemma: left aortic arch with right descending aorta-a rare vascular ring. Pediatr Cardiol 1997; 18: 45–48.CrossRefGoogle ScholarPubMed
4. McKenzie, ED, Roeser, ME, Thompson, JL, et al. Descending aortic translocation for relief of distal tracheal and proximal bronchial compression. Ann Thorac Surg 2016; 102: 859–862.Google Scholar
5. Sanchez Torres, G, RoldanConesa, D. Left aortic arch without a circumflex segment and a right descending aorta: a hypothetical case and a real example. Arch Inst Cardiol Mex 1989; 59: 125–131.Google Scholar
6. Rad, EM, Mortezaeian, H, Pouraliakbar, HR, Hijazi, ZM. Pitfalls of stenting coarctation of an angulated right circumflex aortic arch in Goldenhar syndrome. Ann Pediatr Cardiol 2017; 10: 194–196.Google Scholar
7. Hilmes, M, Hernandez, R, Devaney, E. Markedly hypoplastic circumflex retroesophageal right aortic arch: MR imaging and surgical implications. Pediatr Radiol 2007; 37: 63–67.Google Scholar
8. Humphrey, C, Duncan, K, Fletcher, S. Decade of experience with vascular rings at a single institution. Pediatrics 2006; 117: e903–e908.Google Scholar
9. Berman, W, Yabek, SM, Dillon, T, et al. Vascular ring due to left aortic arch and right descending aorta. Circulation 1981; 63: 458–460.CrossRefGoogle ScholarPubMed
10. McLeary, MS, Frye, LL, Young, LW. Magnetic resonance imaging of a left circumflex aortic arch and aberrant right subclavian artery: the other vascular ring. Pediatr Radiol 1998; 28: 263–265.CrossRefGoogle ScholarPubMed
Supplementary material: Image

Sheth et al. supplementary material 1

Supplementary Figure

Download Sheth et al. supplementary material 1(Image)
Image 5.5 MB
Supplementary material: Image

Sheth et al. supplementary material 2

Supplementary Figure

Download Sheth et al. supplementary material 2(Image)
Image 6.5 MB