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Isomerism of the left atrial appendages associated with bronchoatrial discordance and unusual systemic venous drainage

Published online by Cambridge University Press:  19 August 2008

Francis M. Jewel ,
Hyam S. Joffe  and
Peter Wilde
Francis M. Jewel*
Affiliation:
From the Department of Clinical Radiology, Bristol Children's Hospital, Bristol
Hyam S. Joffe
Affiliation:
Bristol Royal Infirmary and the Department of Cardiology, Bristol Children's Hospital, Bristol
Peter Wilde
Affiliation:
From the Department of Clinical Radiology, Bristol Children's Hospital, Bristol
*
Dr. Francis M. Jewell,Department of Clinical Radiology, Bristol Royal Infirmary, Bristol, BS2 8HW, United Kingdom. Tel. 0272-282731.
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Abstract

A complex case of congenital heart disease is presented which features isomerism of the left atrial appendages combined with bronchoatrial discordance and an anteriorly placed non-interrupted inferior caval vein draining to the left-sided atrium. This combination of anomalies has, as far as we are aware, not been described before. It emphasizes the importance of direct confirmation of atrial arrangement by atrial angiography or transesophageal echocardiography.

Keywords

Isomerismleft atrial appendageanomalous systemic venous return
Type
Brief Reports
Information
Cardiology in the Young , Volume 3 , Issue 3 , July 1993 , pp. 225 - 228
Copyright
Copyright © Cambridge University Press 1993

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