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Isomerism of the left atrial appendages associated with bronchoatrial discordance and unusual systemic venous drainage

Published online by Cambridge University Press:  19 August 2008

Francis M. Jewel ,
Hyam S. Joffe  and
Peter Wilde
Francis M. Jewel*
Affiliation:
From the Department of Clinical Radiology, Bristol Children's Hospital, Bristol
Hyam S. Joffe
Affiliation:
Bristol Royal Infirmary and the Department of Cardiology, Bristol Children's Hospital, Bristol
Peter Wilde
Affiliation:
From the Department of Clinical Radiology, Bristol Children's Hospital, Bristol
*
Dr. Francis M. Jewell,Department of Clinical Radiology, Bristol Royal Infirmary, Bristol, BS2 8HW, United Kingdom. Tel. 0272-282731.
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Abstract

A complex case of congenital heart disease is presented which features isomerism of the left atrial appendages combined with bronchoatrial discordance and an anteriorly placed non-interrupted inferior caval vein draining to the left-sided atrium. This combination of anomalies has, as far as we are aware, not been described before. It emphasizes the importance of direct confirmation of atrial arrangement by atrial angiography or transesophageal echocardiography.

Keywords

Isomerismleft atrial appendageanomalous systemic venous return
Type
Brief Reports
Information
Cardiology in the Young , Volume 3 , Issue 3 , July 1993 , pp. 225 - 228
Copyright
Copyright © Cambridge University Press 1993

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References

1.Sapire, DW. Atrial isomerism In: Anderson, RH, Macartney, FJ, Shinebourne, EA, Tynan, M (eds). Paediarric Cardiology. Churchill Livingstone, Edinburgh, 1987, pp 473–485.Google Scholar
2.Van Praagh, R, Van Praagh, S, VIad, P, Keith, JD. Anatomic types of congenital dextrocardia. Diagnosis and embryologic implications. Am J Cardiol 1964; 13: 510–531.CrossRefGoogle Scholar
3.Macartney, FJ, Zuberbuhler, JR, Anderson, RH. Morphologi cal considerations pertaining to recognition of atrial isomer-ism. Consequences for sequential chamber analysis. Br Heart J 1980; 44: 657–667.CrossRefGoogle Scholar
4.Eluhta, JC, Smalihorn, JF, Macartney, FJ. Two dimensional echocardiographic diagnosis ofsitus. Br Heart J 1982; 48: 97–108.Google Scholar
5.Stumper, OFM, Sreeram, N, Eizenga, NS, Sutherland, GR. Diagnosis ofatrial situs by transesophageal echocardiography. J Am Coil Cardioi 1990; 16: 442–446.CrossRefGoogle Scholar
6.Weinstraub, R, Shiora, T, Elkadi, T, Goiebiorski, P, Zhang, J, Rorhman, A, Ritter, SB, Sahn, DJ. Transesophageai echocardiography in infants and children with congenital heart disease. Circulation 1992; 86: 711–722.Google Scholar
7.Devine, WA. What if Iremark had suggested the term “syn dromeofvisceral symmetrywith aspienia” instead of “asplenia, a teratologic syndrome of visceral heterotaxy”? Cardioi Young 1992; 2: 108–113.CrossRefGoogle Scholar
8.Van Mierop, LHS. Morphological characteristics of the atria and their variations, including characteristics in the splenic syndromes. In: Godman, MJ (ed). Paediatric Cardiology, Vol 4. Churchill Livingstone, Edinburgh, 1981, pp 144–152.Google Scholar
9.Caruso, G, Becker, AE. How to determine atrial situs? Consid erations initiated by three cases of absent spleen with a discordant anatomy between bronchi and atria. Br Heart J 1979; 41: 559–567.CrossRefGoogle Scholar
10.Elliot, LP, Cramer, GC, Amplatz, K. The anomalous relation ship of the inferior vena cava and abdominal aorta as a specific angiocardiographic sign in asplenia. Radiology 1966; 87: 859–863.Google Scholar