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Infantile scimitar syndrome with severe pulmonary hypertension: successful treatment with coil embolization of the systemic arterial supply to the sequestered lung

Published online by Cambridge University Press:  19 August 2008

Jean-Pierre Pfammatter ,
Ingrid Luhmer  and
Hans Carlo Kallfelz
Jean-Pierre Pfammatter*
Affiliation:
Division of Pediatric Cardiology, Children's Hospital, Hannover Medical SchoolHannover, Germany
Ingrid Luhmer
Affiliation:
Division of Pediatric Cardiology, Children's Hospital, Hannover Medical SchoolHannover, Germany
Hans Carlo Kallfelz
Affiliation:
Division of Pediatric Cardiology, Children's Hospital, Hannover Medical SchoolHannover, Germany
*
Dr Jean-Pierre Pfammatter, MD. Division of Pediatric CardiologyChildren's Hospital, Freiburgstrasse, CH-3010 Berne, Switzerland. Fax: ++41 31 632 9748
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Abstract

Scimitar syndrome is a rare cardiopulmonary malformation. Presentation in infancy is usually associated with pulmonary hypertension and severe symptoms. We discuss treatment of such an infant. Two abnormal systemic vessels supplying the sequestered lower part of the right lung were embolized using catheter-inserted coils. The patent arterial duct was surgically ligated. These procedures resulted in a significant reduction of the shunt and the level of pulmonary hypertension, as well as in an impresssive improvement of symptoms.

Keywords

Coil embolizationpulmonary hypertensionscimitar syndrome
Type
Brief-Reports
Information
Cardiology in the Young , Volume 7 , Issue 4 , October 1997 , pp. 454 - 457
Copyright
Copyright © Cambridge University Press 1997

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