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Hepatocellular carcinoma in the adult Fontan patient

Published online by Cambridge University Press:  19 September 2016

Michael R. Conroy Open the ORCID record for Michael R. Conroy [Opens in a new window]  and
Tabitha G. Moe
Michael R. Conroy
Affiliation:
Department of Cardiology, Mayo Clinic, Scottsdale, Arizona, United States of America
Tabitha G. Moe*
Affiliation:
Department of Cardiology, Mayo Clinic, Scottsdale, Arizona, United States of America
*
Correspondence to: Dr T. Moe, Department of Cardiology, Mayo Clinic, Scottsdale, AZ 85054, United States of America. Tel: 480 515 6296; Fax: 602 933 4166; E-mail: [email protected]
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Abstract

In this study, we describe the case of a 36-year-old woman who was diagnosed with hepatocellular carcinoma on a background of Fontan procedure for tricuspid atresia. She had worsening heart failure in the months before presentation, and early investigations noted derangement in liver enzymes and hepatomegaly. Liver biopsy confirmed a hepatocellular carcinoma. Hepatocellular carcinoma is a rare but recognised consequence of cardiac cirrhosis in Fontan patients.

Keywords

Fontanhepatocellularcirrhosisscreening
Type
Brief Report
Information
Cardiology in the Young , Volume 27 , Issue 2 , March 2017 , pp. 407 - 409
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Copyright
© Cambridge University Press 2016 

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