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Fibromuscular dysplasia as the substrate for systemic and pulmonary hypertension in the setting of Moya-Moya disease

Published online by Cambridge University Press:  20 September 2006

Phalla Ou ,
Peggy Dupont  and
Damien Bonnet
Phalla Ou
Affiliation:
Cardiologie Pédiatrique, Hôpital Necker-Enfants Malades, AP-HP, Paris, France
Peggy Dupont
Affiliation:
Cardiologie Pédiatrique, Hôpital Necker-Enfants Malades, AP-HP, Paris, France
Damien Bonnet
Affiliation:
Cardiologie Pédiatrique, Hôpital Necker-Enfants Malades, AP-HP, Paris, France
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Abstract

We report the first case, to the best of our knowledge, of a child with the unusual association of Moya-Moya disease and both systemic and pulmonary hypertension. Histological examination revealed fibromuscular dysplasia as the common denominator for a diffuse arteriopathy.

Keywords

Pulmonary arterial stenosisrenal arterial stenosiscerebrovascular pathology
Type
Brief Report
Information
Cardiology in the Young , Volume 16 , Issue 5 , October 2006 , pp. 495 - 497
Copyright
© 2006 Cambridge University Press

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