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A fatal case of idiopathic restrictive cardiomyopathy

Published online by Cambridge University Press:  24 May 2005

Przemysław Palka ,
Aleksandra Lange  and
Cameron Ward
Przemysław Palka
Affiliation:
St Andrew's Heart Institute & Department of Echocardiography, Prince Charles Hospital Queensland, Australia
Aleksandra Lange
Affiliation:
Department of Pediatric Cardiology Children Mater Hospital, Brisbane, Queensland, Australia
Cameron Ward
Affiliation:
St Andrew's Heart Institute & Department of Echocardiography, Prince Charles Hospital Queensland, Australia
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Abstract

We describe the clinical features of idiopathic restrictive cardiomyopathy in a female infant. A marked elevation of left ventricular end-diastolic pressure, and profoundly abnormal myocardial relaxation, were detected with the use of Doppler blood flow echocardiography, coupled with the relatively new technique of Doppler tissue echocardiography. There was no clinical evidence of ongoing heart failure, but she had signs of myocardial ischaemia, and unfortunately died suddenly at the age of 13 months.

Keywords

Childhood restrictive cardiomyopathydiastolic dysfunctionDoppler tissue echocardiography
Type
Brief Report
Information
Cardiology in the Young , Volume 13 , Issue 5 , October 2003 , pp. 469 - 471
Copyright
© 2003 Cambridge University Press

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References

Siegel RJ, Shah PK, Fishbein MC. Idiopathic restrictive cardio-myopathy. Circulation 1984; 70: 165–169.Google Scholar
Richardson P, McKenna W, Bristow M, et al. Report of the 1995 World Health Organization/International Society and Federation of Cardiology task force on the definition and classification of cardiomyopathies. Circulation 1996; 93: 841–842.Google Scholar
Kushwaha SS, Fallon JT, Fuster V. Restrictive cardiomyopathy. N Engl J Med 1997; 336: 267–276.Google Scholar
Cetta F, O'Leary PW, Seward JB, Driscoll DJ. Idiopathic restrictive cardiomyopathy in childhood: diagnostic features and clinical course. Mayo Clin Proc 1995; 70: 634–640.Google Scholar
Ammash NM, Seward JB, Baily KR, Edwards WD, Tajik AJ. Clinical profile and outcome of idiopathic restrictive cardiomyopathy. Circulation 2000; 101: 2490–2496.Google Scholar
Palka P, Lange A, Donnelly JE, Nihoyannopoulos P. Differentiation between restrictive cardiomyopathy and constrictive pericarditis by early diastolic Doppler myocardial velocity gradient at the posterior wall. Circulation 2000; 102: 655–662.Google Scholar
Nield LE, McCrindle BW, Bohn DJ, et al. Outcomes for children with cardiomyopathy awaiting transplantation. Cardiol Young 2000; 10: 358–366.Google Scholar
Little WC, Ohno M, Kitzman DW, Thomas JD, Cheng CP. Determination of left ventricular chamber stiffness from the time for deceleration of early left ventricular filling. Circulation 1995; 92: 1933–1939.Google Scholar
Gewilling M, Mertens L, Moerman P, Dumoulin M. Idiopathic restrictive cardiomyopathy in childhood. Eur Heart J 1996; 17: 1413–1420.Google Scholar
Rivenes SM, Kearney DL, Smith EO, Towbin JA, Denfield SW. Sudden death and cardiovascular collapse in children with restrictive cardiomyopoathy. Circulation 2000; 102: 876–882.Google Scholar