Hostname: page-component-586b7cd67f-rdxmf Total loading time: 0 Render date: 2024-11-23T17:59:52.495Z Has data issue: false hasContentIssue false
  • English
  • Français

A familial variant of the Scimitar syndrome with a meandering pulmonary vein

Published online by Cambridge University Press:  26 May 2006

Ghassan H. Al-Naami  and
Riyadh M. Abu-Sulaiman
Ghassan H. Al-Naami
Affiliation:
Pediatric Cardiology Division, Cardiac Science Department, King AbdulAziz Medical City, Riyadh, Saudi Arabia
Riyadh M. Abu-Sulaiman
Affiliation:
Pediatric Cardiology Division, Cardiac Science Department, King AbdulAziz Medical City, Riyadh, Saudi Arabia
Get access Rights & Permissions [Opens in a new window]

Abstract

We report a rare variant of the Scimitar syndrome, in which the right lower pulmonary vein takes a meandering course before finally connecting in normal fashion to the left atrium. The pulmonary parenchymal segment drained by the tortuous vein is supplied by a systemic collateral artery, which was coiled via a catheter. We also closed the intracardiac defects by surgery. The elder brother of the patient had classical Scimitar syndrome.

Keywords

Congenital heart diseasevenous returnechocardiographyangiography
Type
Brief Report
Information
Cardiology in the Young , Volume 16 , Issue 3 , June 2006 , pp. 308 - 309
Copyright
© 2006 Cambridge University Press

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

Tortoriello AT, Vick III GW, Chung T, Bezold LI, Vincent JA. Meandering right pulmonary vein to the left atrium and inferior vena cava: the first case with associated anomalies. Tex Heart Inst J 2002; 29: 319–323.Google Scholar
Pearl W. Scimitar variant. Pediatr Cardiol 1987; 8: 139–141.Google Scholar
Ashida K, Itoh A, Noruko T. Familial Scimitar syndrome. Three-dimensional visualization of anomalous pulmonary vein in young sisters. Circulation 2001; 103: E126–E127.Google Scholar
Holt PD, Berdon WE, Marans Z, Griffiths S, Hsu D. Scimitar vein draining to the left atrium and a historical review of the scimitar syndrome. Pediatr Radiol 2004; 34: 409–413.Google Scholar
Kriss VM, Woodring JH, Cottrill CM. “Meandering” pulmonary veins: report of a case in an asymptomatic 12-year-old girl. J Thorac Imaging 1995; 10: 142–145.Google Scholar
Salazar-Mena J, Salazar-Gonzalez J, Salazar-Gonzalez E. Meandering right pulmonary vein: a case of scimitar variant. Pediatr Radiol 1999; 29: 578–580.Google Scholar
Takeda S, Imachi T, Arimitsu K, Minami M, Hayakawa M. Two cases of scimitar variant. Chest 1994; 105: 292–293.Google Scholar
Goodman LR, Jamshidi A, Hipona FA. Meandering right pulmonary vein simulating the Scimitar syndrome. Chest 1972; 62: 510–512.Google Scholar
Saitoh H, Nakamura A, Ohnishi M, Shichijoh Y. [Meandering pulmonary veins] Ryoikibetsu Shokogun Shirizu 1996; 13: 305–307.Google Scholar
Kanemoto N, Sugiyama T, Hirose S, Goto Y. A case with pseudo-scimitar syndrome: “scimitar sign” with normal pulmonary venous drainage. Jpn Circ J 1987; 51: 642–646.Google Scholar