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Endocrinopathies mimicking gene negative long QT syndrome

Part of: Electrophysiology

Published online by Cambridge University Press:  24 November 2021

Praloy Chakraborty Open the ORCID record for Praloy Chakraborty [Opens in a new window] ,
Jason D. Roberts  and
Michael H. Gollob
Praloy Chakraborty
Affiliation:
Inherited Arrhythmia and Cardiomyopathy Program, Toronto General Hospital, University of Toronto, Toronto, Ontario, Canada
Jason D. Roberts
Affiliation:
Section of Cardiac Electrophysiology, Division of Cardiology, Western University, London, Ontario, Canada Population Health Research Institute, McMaster University, and Hamilton Health Sciences, Hamilton, Ontario, Canada
Michael H. Gollob*
Affiliation:
Inherited Arrhythmia and Cardiomyopathy Program, Toronto General Hospital, University of Toronto, Toronto, Ontario, Canada Inherited Arrhythmia and Cardiomyopathy Clinic, Partners in Advanced Cardiac Evaluation, Newmarket, Ontario, Canada
*
Author for correspondence: M. H. Gollob, MD, Inherited Arrhythmia and Cardiomyopathy Clinic, Toronto General Hospital, 200 Elizabeth St, Toronto, Ontario, Canada, M5G 2C4. Tel: 416-340-4282; Fax: 416-340-3281. E-mail: [email protected]
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Abstract

Ventricular repolarisation can be influenced by hormonal milieu which may mimic long QT syndrome. We describe a series of patients referred for genetic testing for diagnosed long QT syndrome where a detailed clinical workup demonstrated endocrinopathies as the cause of presumed “gene negative” long QT syndrome and QT prolongation.

Keywords

Long QT syndromecardiac arrestendocrinopathygeneticsadrenal crisis
Type
Brief Report
Information
Cardiology in the Young , Volume 32 , Issue 6 , June 2022 , pp. 1016 - 1018
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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References

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