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Ectopic accessory liver masquerading as spleen in a case with isomerism of the right atrial appendages

Published online by Cambridge University Press:  19 August 2008

Siew Yen Ho*
Affiliation:
From the Department of Paediatrics, Royal Brompton and National Heart ' Lung Hospital, London.
Simon E. Trotter
Affiliation:
National Heart & Lung Institute, London and the Departments of Pathology, Royal Brompton and National Heart ' Lung Hospital, London
Andrew N. Redington
Affiliation:
and Paediatrics, Royal Brompton and National Heart ' Lung Hospital, London
*
Dr. Siew Yen Ho, Department of Paediatrics, National Heart & Lung Institute, Dovehouse Street, London SW3 6LY, United Kingdom. Tel. 71-351-8894; Fax. 71-352-0032.

Summary

We report a case of an infant with isomerism of the right atrial appendages in whom a spleen-like nodule was found at post-mortem. The nodule, on histology, was found to be a fragment of liver. The cardiac lesions were typical of those associated with right isomerism, a complex generally described as the “asplenia syndrome.” The presence of either a spleen, or a nodule masquerading as a spleen, does not preclude an isomeric arrangement of the atrial appendages nor its commonly associated constellation of cardiovascular anomalies.

Type
Brief Reports
Copyright
Copyright © Cambridge University Press 1993

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