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Ectopic accessory liver masquerading as spleen in a case with isomerism of the right atrial appendages

Published online by Cambridge University Press:  19 August 2008

Siew Yen Ho ,
Simon E. Trotter  and
Andrew N. Redington
Siew Yen Ho*
Affiliation:
From the Department of Paediatrics, Royal Brompton and National Heart ' Lung Hospital, London.
Simon E. Trotter
Affiliation:
National Heart & Lung Institute, London and the Departments of Pathology, Royal Brompton and National Heart ' Lung Hospital, London
Andrew N. Redington
Affiliation:
and Paediatrics, Royal Brompton and National Heart ' Lung Hospital, London
*
Dr. Siew Yen Ho, Department of Paediatrics, National Heart & Lung Institute, Dovehouse Street, London SW3 6LY, United Kingdom. Tel. 71-351-8894; Fax. 71-352-0032.
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Summary

We report a case of an infant with isomerism of the right atrial appendages in whom a spleen-like nodule was found at post-mortem. The nodule, on histology, was found to be a fragment of liver. The cardiac lesions were typical of those associated with right isomerism, a complex generally described as the “asplenia syndrome.” The presence of either a spleen, or a nodule masquerading as a spleen, does not preclude an isomeric arrangement of the atrial appendages nor its commonly associated constellation of cardiovascular anomalies.

Keywords

Right isomerismectopic liverright atrial appendages
Type
Brief Reports
Information
Cardiology in the Young , Volume 3 , Issue 1 , January 1993 , pp. 43 - 46
Copyright
Copyright © Cambridge University Press 1993

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