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Early onset of progressive subaortic stenosis after complete repair of tetralogy of Fallot

Published online by Cambridge University Press:  19 August 2008

Victor Grech  and
Anton Mifsud
Victor Grech*
Affiliation:
St. Luke's Hospital, Guardamangia, Malta
Anton Mifsud
Affiliation:
St. Luke's Hospital, Guardamangia, Malta
*
Victor Grech, Paediatric Senior Registrar, St. Luke's Hospital, Guardamangia, Malta. Tel: + 356 241251 Ext: 1471; Fax: +356 240176; E-mail: [email protected]
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Abstract

Tetralogy of Fallot is often found in association with a wide variety of other cardiac lesions, but is rarely found in association with lesions causing obstruction to the left ventricular inflow or outflow. Subaortic stenosis has only rarely been reported in association with tetralogy of Fallot. We report a patient with Marfan syndrome who underwent repair of tetralogy of Fallot at five years of age. Discrete and progressive subaortic stenosis developed two years after the surgical correction, in a previously normal and unobstructed left ventricular outflow tract. Surgical removal of the acquired fibrous subaortic shelf was successful. Clinical signs of obstruction within the left ventricular outflow tract after surgical repair of tetralogy of Fallot should prompt further investigation to exclude the onset of acquired subaortic stenosis.

Keywords

Heart defectscongenitaltetralogy of Fallotsubaortic stenosisdiscreteMarfan syndrome
Type
Brief Reports
Information
Cardiology in the Young , Volume 10 , Issue 1 , January 2000 , pp. 57 - 59
Copyright
Copyright © Cambridge University Press 2000

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