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Double outlet right atrium and complete atrioventricular septal defect with abnormal findings of the biopsied lung

Published online by Cambridge University Press:  19 August 2008

Kiyoshi Suzuki ,
Toshio Kikuchi  and
Shigekazu Mimori
Kiyoshi Suzuki*
Affiliation:
From the Departments of Pediatric Cardiology and Cardiac Surgery, Sakakibara Heart Institute, Tokyo.
Toshio Kikuchi
Affiliation:
From the Departments of Pediatric Cardiology and Cardiac Surgery, Sakakibara Heart Institute, Tokyo.
Shigekazu Mimori
Affiliation:
From the Departments of Pediatric Cardiology and Cardiac Surgery, Sakakibara Heart Institute, Tokyo.
*
Dr. Kiyoshi Suzuki, Department of Pediatric Cardiology, Sakakibara Heart Institute, 2-5-4 Yoyogi, Shibuya-ku, Tokyo 151, Japan. Tel. 3-3375-3111; Fax. 3-3375-9218.
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Summary

We describe a rare type of atrioventricular septal defect with common atrioventricular orifice and malaligned atrial septum, the latter feature resulting in severe obstruction of the left atrial egress. Excision of the atrial septum and banding of the pulmonary trunk was performed at the age of thirteen months. Lung biopsy demonstrated marked medial hypertrophy with severe intimal fibrosis in the small pulmonary arteries and mild thickening of the pulmonary veins, considered contraindications for corrective surgery.

Keywords

Atrioventricular septal defectdouble outlet right atriumlung biopsypulmonary venous obstruction
Type
Brief Reports
Information
Cardiology in the Young , Volume 4 , Issue 4 , October 1994 , pp. 402 - 404
Copyright
Copyright © Cambridge University Press 1994

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