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Double outlet left atrium with co-existing double inlet left ventricle and discordant atrioventricular connections

Published online by Cambridge University Press:  19 August 2008

James P. Gnanapragasam*
Affiliation:
Department of Cardiology, Royal Hospital for Sick Children, Glasgow and the National Heart & Lung Institute, University of London, London
Allan B. Houston
Affiliation:
Department of Cardiology, Royal Hospital for Sick Children, Glasgow and the National Heart & Lung Institute, University of London, London
Robert H. Anderson
Affiliation:
Department of Cardiology, Royal Hospital for Sick Children, Glasgow and the National Heart & Lung Institute, University of London, London
*
Dr. James P. Gnanapragasam, Department of Cardiology, Royal Hospital for Sick Children, Glasgow, G3 8SJ, United Kingdom

Summary

We describe an unusual heart in which double outlet from the left atrium resulted in atrioventricular connections to a dominant left ventricle and to a left-sided rudimentary right ventricle, while the right atrium also connected to the left ventricle. This produced, in effect, double inlet left ventricle in association with discordant atrioventricular connections. The diagnosis was made by echocardiography and confirmed at post mortem examination.

Type
Brief Reports
Copyright
Copyright © Cambridge University Press 1991

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References

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