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Divided left atrium associated with supravalvar mitral ring

Published online by Cambridge University Press:  19 August 2008

Silvia Álvares*
Affiliation:
Pediatric Cardiology Unit, Children's Hospital Maria Pia, Porto, Portugal
António Sá Melo
Affiliation:
Pediatric Cardiology Unit Coimbra, Portugal
Manuel Antunes
Affiliation:
Cardiothoracic Surgery Department, University Hospital, Coimbra, Portugal
*
Silvia Álvares, Consultant, Hospital de Crianças Maria Pia, Rua da Boavista 827, P–4050 Porto, Portugal. Tel: 026089900; Fax: 026000841

Abstract

Reported is a case with a rare association of divided left atrium, supramitral stenosing ring of the left atrium, connection of the left superior caval vein to the roof of the left atrium, unroofed coronary sinus with an interatrial communication at the mouth of the unroofed sinus and ventricular septal defect. The need for a complete echocardiographic examination in the presence of pulmonary venous obstruction is emphasized. Surgery was successful in spite of significant preoperative pulmonary hypertension.

Type
Brief Reports
Copyright
Copyright © Cambridge University Press 1999

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