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Discordant atrioventricular and ventriculoarterial connections with partially unguarded left-sided atrioventricular orifice and aortic atresia

Published online by Cambridge University Press:  19 August 2008

Matthias Freund ,
Achim Magener  and
Klaus G. Schmidt
Matthias Freund
Affiliation:
From the Department of Pediatric Cardiology, University Children's Hospital, University of Heidelberg, Germany
Achim Magener
Affiliation:
From the Department of Pediatric Cardiology, The Institute of Pathology, University of Heidelberg, Germany
Klaus G. Schmidt*
Affiliation:
From the Department of Pediatric Cardiology, University Children's Hospital, University of Heidelberg, Germany
*
Klaus G. Schmidt, M.D. Department of Pediatric Cardiology, University Children's Hospital, Im Neuenheimer Feld 150, 69120 Heidelberg, F.R.G. Tel. 49-6221-562311, Fax 49-6221-565790
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Abstract

Congenitally unguarded morphologically tricuspid valvar orifice is a rare abnormality, usually associated with pulmonary atresia. We describe such a case found in association with discordant atrioventricular and ventriculoarterial connections in which the aortic valve was atretic. Presentation was with respiratory distress due to severe cardiac failure after birth. Echocardiography demonstrated a dilated systemic ventricle with poor function, left atrial enlargement, and aortic atresia. The clinical findings were confirmed at autopsy.

Keywords

Unguarded tricuspid valvar orificeaortic valvar atresiaEbstein's malformation
Type
Brief-Reports
Information
Cardiology in the Young , Volume 7 , Issue 4 , October 1997 , pp. 450 - 453
Copyright
Copyright © Cambridge University Press 1997

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