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Diaphragmatic eventration as a first sign of Scimitar syndrome

Published online by Cambridge University Press:  04 May 2021

Miguel Vieira Martins*
Affiliation:
Pediatrics Department, Centro Hospitalar Universitario Cova da Beira, Covilha, Portugal
Duarte S Martins
Affiliation:
Pediatric Cardiology Department, Hospital Santa Cruz, Centro Hospitalar Lisboa Ocidental, Carnaxide, Portugal
Graça Oliveira
Affiliation:
Neonatology Department, Hospital Santa Maria, Centro Hospitalar Universitário Lisboa Norte, Lisboa, Portugal
*
Author for correspondence: Miguel Vieira Martins, M.D., Pediatrics Department, Centro Hospitalar Universitario Cova da Beira, Quinta do Alvito, 6200-251Covilha, Castelo Branco, Portugal. Tel: +351 275 330 000. E-mail:[email protected]

Abstract

Diaphragmatic eventration is an anomaly of the diaphragm. In Scimitar syndrome, a curved-shaped anomalous pulmonary venous drainage is seen. Association between these conditions is rare. We present a newborn with diaphragmatic eventration, whose diagnosis of Scimitar syndrome was made after surgical repair. Scimitar syndrome is a congenital disorder often associated with other heart and lungs anomalies. Diagnosis can be fortuitous but with important prognostic features.

Type
Brief Report
Copyright
© The Author(s), 2021. Published by Cambridge University Press

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