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Diagnosis and natural history of isolated congenital pulmonary regurgitation in fetal life

Published online by Cambridge University Press:  19 August 2008

Kazuhiro Mori ,
Yasunobu Hayabuchi  and
Yasuhiro Kuroda
Kazuhiro Mori*
Affiliation:
Department of Pediatrics, School of Medicine, University of Tokushima, Tokushima, Japan
Yasunobu Hayabuchi
Affiliation:
Department of Pediatrics, School of Medicine, University of Tokushima, Tokushima, Japan
Yasuhiro Kuroda
Affiliation:
Department of Pediatrics, School of Medicine, University of Tokushima, Tokushima, Japan
*
Kazuhiro Mori, MD, Department of Pediatrics, School of Medicine, University of Tokushima, 3–18–15 Kuramoto-cho, Tokushima-city, Tokushima, 770–8503, Japan Tel. 81–886–33–7135, Fax: 81–886–31–8697
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Abstract

We describe a rare instance of isolated pulmonary regurgitation caused by a dysplastic pulmonary valve which was detected prenatally. Fetal echocardiography demonstrated severe pulmonary regurgitation, and progressive cardiomegaly because of right ventricular volume overload. After birth, conservative therapy was successful in alleviating the pulmonary vascular resistance, and the pulmonary regurgitation gradually decreased.

Keywords

Congenital pulmonary regurgitationdysplastic pulmonary valvefetal echocardiography
Type
Brief Reports
Information
Cardiology in the Young , Volume 10 , Issue 2 , March 2000 , pp. 162 - 165
Copyright
Copyright © Cambridge University Press 2000

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References

1.Berman, W, Fripp, RR, Rowe, SA, Yabek, SM. Congenital isolated pulmonary valve incompetence: neonatal presentation and early natural history. Am Heart J 1992; 124: 248–251.CrossRefGoogle ScholarPubMed
2.Ito, T, Engle, MA, Holswade, GR. Congenital insufficiency of the pulmonic valve: a rare cause of neonatal heart failure. Pediatrics 1961: 28; 712–718.CrossRefGoogle Scholar
3.Lau, K, Cheung, HH, Mok, C. Congenital absence of the pulmonary valve, intact interventriculat septum, and patent ductus arteriosus: Management in a newborn infant. Am Heart J 1990: 120; 711–714.CrossRefGoogle Scholar
4.Thanopoulos, BD, Fisher, EA, Hastreiter, AR. Large ductus arte riosus and intact ventricular septum associated with congenital absence of the pulmonary valve. Br Heart J 1986; 55: 602–604.CrossRefGoogle Scholar
5.Horigome, H, Sakakibara, Y, Asumi, N, Miyamoto, T, Sato, H. Absent pulmonary valve with intact ventricular septum presenting as cardiorespiratory failure at birth. Pediatr Cardiol 1997; 18: 136–138.CrossRefGoogle ScholarPubMed
6.Tamura, M, Miyasaka, K. High frequency ventilation. Lancet 1991; 337: 1354–1355.CrossRefGoogle ScholarPubMed
7.Tulzer, G, Gudmundsson, S, Sharkey, AM, Wood, DC, Cohen, AW, Huhtaj, C. Doppler echocardiography of fetal ductus arte riosus constriction versus increased right ventricular output. J Am Coil Cardiol 1991; 18: 532–536.CrossRefGoogle Scholar
8.Emmanouilides, GC, Thanopoulos, B, Siassi, B, Fishbein, M. “Agenesis” of the ductus arteriosus associated with the syndrome of tetralogy of Fallot and absent pulmonary valve. AmJ Cardiol 1976; 37: 403–409.CrossRefGoogle Scholar
9.Smrcek, JM, Germer, U, Gembruch, U. Functional pulmonary valve regurgitation in the fetus. Ultrasound Obstet Gynecol 1998; 12: 254–259.CrossRefGoogle ScholarPubMed