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Cor triatriatum sinister with an intact interatrial septum and a decompressing vein in a toddler

Published online by Cambridge University Press:  06 March 2017

Ziyad M. Binsalamah ,
Luis E. De León  and
Jeffrey S. Heinle
Ziyad M. Binsalamah*
Affiliation:
Division of Congenital Heart Surgery, Texas Children’s Hospital, Houston, TX, United States of America Michael E. DeBakey Department of Surgery, Baylor College of Medicine, Houston, TX, United States of America
Luis E. De León
Affiliation:
Division of Congenital Heart Surgery, Texas Children’s Hospital, Houston, TX, United States of America Michael E. DeBakey Department of Surgery, Baylor College of Medicine, Houston, TX, United States of America
Jeffrey S. Heinle
Affiliation:
Division of Congenital Heart Surgery, Texas Children’s Hospital, Houston, TX, United States of America Michael E. DeBakey Department of Surgery, Baylor College of Medicine, Houston, TX, United States of America
*
Correspondence to: Z. M. Binsalamah, MD, MSc, Division of Congenital Heart Surgery, Texas Children’s Hospital; Michael E. DeBakey Department of Surgery, Baylor College of Medicine, 6621 Fannin St, MC19345H, Houston, TX 77030, United States of America. Tel: +1 832 826 1929; Fax: +1 832 825 1905; E-mail: [email protected]
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Abstract

Cor triatriatum sinister is a very rare cardiac anomaly that may lead to pulmonary hypertension, right ventricular dilation, and eventually right heart failure. We report a case of a toddler who presented with respiratory distress and cardiomegaly and was found to have cor triatriatum sinister with a restrictive communication, decompressing vertical vein, pulmonary hypertension, severe tricuspid regurgitation, and severe right ventricular dysfunction. She underwent a successful surgical repair, with normalisation of right ventricular function and pulmonary artery pressure.

Keywords

Cor triatriatumdecompressing vertical veintricuspid regurgitationintact interatrial septumpersistent levoatrial cardinal vein
Type
Brief Report
Information
Cardiology in the Young , Volume 27 , Issue 6 , August 2017 , pp. 1221 - 1224
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Copyright
© Cambridge University Press 2017 

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