Hostname: page-component-586b7cd67f-t7czq Total loading time: 0 Render date: 2024-11-23T07:53:32.642Z Has data issue: false hasContentIssue false
  • English
  • Français

A “congenitally corrected” variant of Ebstein’s anomaly

Part of: Cardiac Morphology

Published online by Cambridge University Press:  10 January 2018

Rengin Çetin Güvenç ,
Gökmen Akgün  and
Tolga S. Güvenç
Rengin Çetin Güvenç
Affiliation:
Department of Cardiology, Dr. Siyami Ersek Cardiovascular and Thoracic Surgery Research and Training Hospital, Istanbul, Turkey
Gökmen Akgün
Affiliation:
Department of Pediatric Cardiology, Dr. Siyami Ersek Cardiovascular and Thoracic Surgery Research and Training Hospital, Istanbul, Turkey
Tolga S. Güvenç*
Affiliation:
Department of Cardiology, Dr. Siyami Ersek Cardiovascular and Thoracic Surgery Research and Training Hospital, Istanbul, Turkey
*
Correspondence to: T. S. Güvenç, Dr. Siyami Ersek Cardiovascular and Thoracic Surgery Research and Training Hospital, Tıbbiye Street No:13, Kadıköy, Istanbul, Turkey. Tel: +90 216 632 1818; Fax: +90 216 632 7124; E-mail: [email protected]
Get access Rights & Permissions [Opens in a new window]

Abstract

Ebstein’s anomaly is a rare CHD that is characterised by caudal displacement of the functional tricuspid annulus and a dysfunctional tricuspid valve owing to a failure of proper leaflet coaptation. We present a balanced variant of Ebstein’s anomaly, in which the overgrowth of the septal leaflet had allowed proper coaptation of the tricuspid leaflets, thus preserving the valve function.

Keywords

Ebstein’s anomalytricuspid valveCHD
Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 4 , April 2018 , pp. 608 - 610
Check for updates
Copyright
© Cambridge University Press 2018 

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1. Lupo, PJ, Langlois, PH, Mitchell, LE. Epidemiology of Ebstein’s anomaly: prevalence and patterns in Texas, 1999-2005. Am J Med Genet A 2011; 155A: 1007–1014.Google Scholar
2. Pradat, P, Francannet, C, Harris, JA, Robert, E. The epidemiology of cardiovascular defects, part I: a study based on data from three large registries of congenital malformations. Pediatr Cardiol 2003; 24: 195–221.Google Scholar
3. Booker, OJ, Nanda, NC. Echocardiographic assessment of Ebstein’s anomaly. Echocardiography 2015; 32 (Suppl 2): S177–S188.Google Scholar
4. Morray, B. Preoperative physiology, imaging, and management of Ebstein’s anomaly of the tricuspid valve. Semin Cardiothorac Vasc Anesth 2016; 20: 74–81.Google Scholar
5. Krieger, EV, Valente, AM. Diagnosis and management of Ebstein’s anomaly of the tricuspid valve. Curr Treat Options Cardiovasc Med 2012; 14: 594–607.Google Scholar
6. Tsujii, N, Kurosaki, K, Yasuda, K, et al. Displacement of the anterior leaflet of the tricuspid valve: rare variant of Ebstein’s anomaly. Pediatr Int. 2016; 58: 775–777.Google Scholar
7. Ammash, NM, Warnes, CA, Connolly, HM, Danielson, GK, Seward, JB. Mimics of Ebstein’s anomaly. Am Heart J 1997; 134: 508–513.Google Scholar

Güvenç et al. supplementary material 1

Supplementary Video

Download Güvenç et al. supplementary material 1(Video)
Video 2.4 MB

Güvenç et al. supplementary material 2

Supplementary Video

Download Güvenç et al. supplementary material 2(Video)
Video 1.3 MB