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Challenges in the primary prevention of sudden cardiac death in hypertrophic cardiomyopathy in the young

Published online by Cambridge University Press:  06 July 2021

Hirokuni Yamazawa*
Affiliation:
Department of Pediatrics, Faculty of Medicine and Graduate School of Medicine, Hokkaido University, Hokkaido, Japan
Atsuhito Takeda
Affiliation:
Department of Pediatrics, Faculty of Medicine and Graduate School of Medicine, Hokkaido University, Hokkaido, Japan
Gaku Izumi
Affiliation:
Department of Pediatrics, Faculty of Medicine and Graduate School of Medicine, Hokkaido University, Hokkaido, Japan
*
Author for correspondence: Hirokuni Yamazawa, MD, PhD, Department of Pediatrics, Faculty of Medicine and Graduate School of Medicine, Hokkaido University, North 15 West 7, Kitaku Sapporo, Hokkaido 060-8638 Japan. Tel: 81 11 706 5954; Fax: 81 11 706 7898. E-mail: [email protected]

Abstract

A case of hypertrophic cardiomyopathy in the transition from childhood to adulthood, which was low risk by the conventional risk assessment model, medium risk by the adult risk prediction model, and high risk by the paediatric risk prediction model, was inserted an implantable cardioverter-defibrillator. Three years post-implantation, the patient was resuscitated with an appropriate discharge of cardioverter-defibrillator.

Type
Brief Report
Copyright
© The Author(s), 2021. Published by Cambridge University Press

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References

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