Hostname: page-component-cd9895bd7-q99xh Total loading time: 0 Render date: 2024-12-24T13:42:47.907Z Has data issue: false hasContentIssue false
  • English
  • Français

Cardiac resynchronisation therapy associated with pulmonary artery banding in an adult with severe right ventricular dysfunction after Mustard repair for complete transposition of the great arteries: results after 2 years of follow-up

Published online by Cambridge University Press:  12 February 2013

Luca Donazzan ,
Giovanni Stellin ,
Werner Guenther Rauhe ,
Lucio Bonazza ,
Josef Stuefer ,
Cristina Romeo  and
Roberto Crepaz
Luca Donazzan*
Affiliation:
Department of Cardiology, San Maurizio Regional Hospital, Bolzano, Italy
Giovanni Stellin
Affiliation:
Pediatric and Congenital Cardiac Surgical Unit, University of Padua, Padua, Italy
Werner Guenther Rauhe
Affiliation:
Department of Cardiology, San Maurizio Regional Hospital, Bolzano, Italy
Lucio Bonazza
Affiliation:
Department of Pneumology, San Maurizio Regional Hospital, Bolzano, Italy
Josef Stuefer
Affiliation:
Service of Radiology, San Maurizio Regional Hospital, Bolzano, Italy
Cristina Romeo
Affiliation:
Department of Cardiology, San Maurizio Regional Hospital, Bolzano, Italy
Roberto Crepaz
Affiliation:
Department of Cardiology, San Maurizio Regional Hospital, Bolzano, Italy
*
Correspondence to: Dr Luca Donazzan, MD, Department of Cardiology, San Maurizio Regional Hospital, Via L. Boehler 5, 39100 Bolzano, Italy. Tel: +390471909985; Fax: +390471909997; E-mail: [email protected]
Get access Rights & Permissions [Opens in a new window]

Abstract

Late dysfunction of the systemic right ventricle in patients with complete transposition of the great arteries after Mustard or Senning procedures and progressive deterioration of the clinical status has been demonstrated. However, evidence-based data on the effective therapy for systemic right ventricular dysfunction in these patients are yet to be defined. Our patient shows an improvement in the right ventricular systolic function, with a reduction in tricuspid regurgitation and a consequent better exercise tolerance after a hybrid approach consisting of an upgrading of a previous transvenous-implanted dual-chamber Implantable Cardiac Defibrillator to biventricular pacing associated with pulmonary artery banding via an anterior thoracotomy.

Keywords

Complete transposition of the great arteriescardiac resynchronisation therapycongestive cardiac failureechocardiography
Type
Original Articles
Information
Cardiology in the Young , Volume 24 , Issue 1 , February 2014 , pp. 99 - 104
Copyright
Copyright © Cambridge University Press 2013 

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1. Dos, L, Tereul, L, Ferreira, IJ, et al. Late outcome of Senning and Mustard procedures for correction of transposition of the great arteries. Heart 2005; 91: 652–656.CrossRefGoogle ScholarPubMed
2. Moons, P, Gewilling, M, Slysmans, T. et al. Long term outcome up to 30 years after the Mustard or Senning operation: a nationwide multicentre study in Belgium. Heart 2004; 90: 307–313.CrossRefGoogle ScholarPubMed
3. Ross-Hesselink, JW, Meijboom, FJ, Spitaels, SE, et al. Decline in ventricular function and clinical condition after Mustard repair for transposition of the great arteries (a prospective study of 22–29 years). Eur Heart J 2004; 25: 1264–1270.CrossRefGoogle Scholar
4. Janousek, J, Tomek, V, Chaloupecky, VA, et al. Cardiac resynchronization therapy: a novel adjunct to the treatment and prevention of systemic right ventricular failure. J Am Coll Cardiol 2004; 44: 964–968.CrossRefGoogle Scholar
5. Dubin, AM, Janousek, J, Rhee, E, et al. Resynchronization therapy in pediatric and congenital heart disease patients: an international multicenter study. J Am Coll Cardiol 2005; 46: 2277–2283.Google Scholar
6. Strieper, M, Krapawich, P, Frias, P, et al. Initial experience with cardiac resynchronization therapy for ventricular dysfunction in young patients with surgically operated congenital heart disease. Am J Cardiol 2004; 94: 1352–1354.Google Scholar
7. Thambo, JB, Bordachar, P, Garrigue, S, et al. Detrimental ventricular remodeling in patients with congenital complete heart block and chronic right ventricular apical pacing. Circulation 2004; 110: 3766–3772.CrossRefGoogle Scholar
8. Chow, PC, Liang, XC, Lam, WM, Cheung, WY, Wong, KT, Cheung, YF. Mechanical right ventricular dyssynchrony in patients after atrial switch operation for transposition of the great arteries. Am J Cardiol 2008; 101: 874–881.Google Scholar
9. Lubizewska, B, Gosiewska, E, Hoffmann, P, et al. Myocardial perfusion and function of the systemic right ventricle in patients after atrial switch procedure for complete transposition: long-term follow-up. J Am Coll Cardiol 2000; 36: 1365–1370.CrossRefGoogle Scholar
10. Singh, TB, Humes, RA, Muzik, O, Kottamasu, S, Karpawich, PP, Di Carli, MF. Myocardial flow reserve in patients with a systemic right ventricle after atrial switch repair. J Am Coll Cardiol 2001; 37: 2120–2125.Google Scholar
11. Babu-Narayan, SV, Goktekin, O, Moon, JC, et al. Late gadolinium enhancement cardiovascular magnetic resonance of the systemic right ventricle in adults with previous atrial redirection surgery for transposition of the great arteries. Circulation 2005; 111: 2091–2098.Google Scholar
12. Giardini, A, Lovato, L, Donti, A, et al. Relation between right ventricular structural alterations and markers of adverse outcome in adults with systemic right ventricle and either congenitally complete (after Senning operation) or congenitally corrected transposition of great arteries. Am J Cardiol 2006; 98: 1277–1282.Google Scholar
13. Gatzoulis, MA, Walters, J, McLaughlin, PR, Merchant, N, Webb, GD, Liu, P. Late arrhythmia in adults with the Mustard procedure for transposition of great arteries: a surrogate marker for right ventricular dysfunction. Heart 2000; 84: 409–415.Google Scholar
14. Cowburn, PJ, Parker, JD, Cameron, DDA, Harris, L. Cardiac resynchronization therapy: retiming the failing right ventricle. J Cardiovasc Electrophysiol 2005; 16: 439–443.CrossRefGoogle ScholarPubMed
15. Bristow, MR, Feldmann, AM, Saxon, LA. Heart failure management using implantable devices for ventricular resynchronization: comparison of medical therapy, pacing and defibrillation in chronic heart failure (COMPANION) trial. COMPANION Steering Committee and COMPANION clinical investigators. J Card Fail 2000; 6: 276–285.CrossRefGoogle Scholar
16. Abraham, WT, Fisher, WG, Smith, AL, et al. Cardiac resynchronization in chronic heart failure. N Eng J Med 2002; 346: 1902–1905.Google Scholar
17. Baumgartner, H, Bonhoeffer, P, De Groot, NM, et al. Task Force on the Management of Grown-up Congenital Heart Disease of the European Society of Cardiology (ESC); Association for European Paediatric Cardiology (AEPC). ESC Guidelines for the management of grown-up congenital heart disease. Eur Heart J 2010; 31: 2915–2957.Google Scholar
18. Cochrane, AD, Karl, TR, Mee, RB. Staged conversion to arterial switch for late failure of the systemic right ventricle. Ann Thorac Surg 1993; 56: 854–861.CrossRefGoogle ScholarPubMed
19. Oechslin, EN, Harrison, DA, Connelly, MS, Webb, GD, Siu, SC. Mode of death in adults with congenital heart disease. Am J Cardiol 2000; 86: 1111–1116.Google Scholar
20. Zipes, DP, Cam, AJ, Borggrefe, M, et al. ACC/AHA/ESC 2006 guidelines for management of patients with ventricular arrhythmias and the prevention of sudden cardiac death. Eur Heart J 2006; 27: 2099–2140.Google Scholar
21. Sutherland, GR, Kukulski, T, Kvitting, JE, et al. Quantitation of left ventricular asynergy by cardiac ultrasound. Am J Cardiol 2004; 86 (Suppl): 4G–9G.Google Scholar
22. Uemura, H, Ho, SY, Anderson, RH, et al. Surgical anatomy of the coronary circulation in hearts with discordant atrioventricular connections. Eur J Cardiothorac Surg 1996; 10: 194–200.Google Scholar
23. Wittig, JH, De Leval, MR, Stark, J. Intraoperative mapping of atrial activation before, during, and after the Mustard operation. J Thorac Cardiovasc Surg 1977; 73: 1–13.CrossRefGoogle ScholarPubMed