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Anomalous origin of the right pulmonary artery from the ascending aorta accompanied by absent pulmonary valve syndrome and right-sided aortic arch: a rare case in adult congenital heart disease

Published online by Cambridge University Press:  01 July 2014

Zahra Khajali
Affiliation:
Fellowship of Echocardiography, Echocardiography Department, Rajaie Cardiovascular, Medical and Research Center, Iran University of Medical Sciences, Tehran, IR Iran
Ali Mohammadzadeh
Affiliation:
Fellowship of Echocardiography, Echocardiography Department, Rajaie Cardiovascular, Medical and Research Center, Iran University of Medical Sciences, Tehran, IR Iran
Marzieh Khayatzadeh*
Affiliation:
Fellowship of Echocardiography, Echocardiography Department, Rajaie Cardiovascular, Medical and Research Center, Iran University of Medical Sciences, Tehran, IR Iran
*
Correspondence to: Dr M. Khayatzadeh, MD; Fellowship of Echocardiography, Echocardiography Department, Rajaie Cardiovascular, Medical and Research Center, Iran University of Medical Sciences, Tehran 1996911151, IR Iran. Tel: +989123276710; Fax: +982122055594; E-mail: [email protected]

Abstract

We present a rare congenital heart disease in a 20-year-old man with anomalous origin of the right pulmonary artery from the ascending aorta, accompanied by absent pulmonary valve syndrome, and a right-sided aortic arch suspected initially in transthoracic echocardiography and subsequently confirmed by cardiac catheterisation and computed tomography angiography.

Type
Brief Reports
Copyright
© Cambridge University Press 2014 

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