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An extensive long term follow-up of a cohort of patients with hypoplasia of the left heart

Published online by Cambridge University Press:  22 December 2006

Petter S. Hagemo ,
Anne-Britt Skarbø ,
Magnhild Rasmussen ,
Per Morten Fredriksen  and
Stein Schage
Petter S. Hagemo
Affiliation:
Department of Pediatric Cardiology, Section for Neurology, Department of Physiotherapy and Section for Child and Adolescent Psychiatry, Rikshospitalet, Oslo, Norway
Anne-Britt Skarbø
Affiliation:
Department of Pediatric Cardiology, Section for Neurology, Department of Physiotherapy and Section for Child and Adolescent Psychiatry, Rikshospitalet, Oslo, Norway
Magnhild Rasmussen
Affiliation:
Department of Pediatric Cardiology, Section for Neurology, Department of Physiotherapy and Section for Child and Adolescent Psychiatry, Rikshospitalet, Oslo, Norway
Per Morten Fredriksen
Affiliation:
Department of Pediatric Cardiology, Section for Neurology, Department of Physiotherapy and Section for Child and Adolescent Psychiatry, Rikshospitalet, Oslo, Norway
Stein Schage
Affiliation:
Department of Pediatric Cardiology, Section for Neurology, Department of Physiotherapy and Section for Child and Adolescent Psychiatry, Rikshospitalet, Oslo, Norway
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Abstract

We report the results of follow-up of the complete cohort of Norwegian children born in the period from 1987 through 1998 in whom there was the intention to treat surgically hypoplasia of the left heart using the Norwood sequence of operations. Of the 54 children, 21 are alive. Of these, 15 have been extensively studied, while the medical state of all the remaining survivors is known from reports from other hospitals. Of the survivors, the majority have reasonably acceptable cardiac and haemodynamic function, but significant neurological and neuropsychological morbidity is identified within the group as a whole, which requires special attention from qualified personnel of various kinds.

Keywords

Congenital heart defectsequelshypoplastic left heart syndrome
Type
Original Article
Information
Cardiology in the Young , Volume 17 , Issue 1 , February 2007 , pp. 51 - 55
Copyright
2007 Cambridge University Press

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