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‘Absent pulmonary valve’ syndrome associated with muscular ventricular septal defect and aneurysmal dilation of the ascending aorta

Published online by Cambridge University Press:  19 August 2008

Dennis Kececioglu
Affiliation:
From the King Faisal Specialist Hospital and Research Center, Riyadh
Omar Galal*
Affiliation:
From the King Faisal Specialist Hospital and Research Center, Riyadh
Fuad Abbag
Affiliation:
From the King Faisal Specialist Hospital and Research Center, Riyadh
*
Dr. Omar Galal, Section of Pediatric Cardiology, Cardiovascular Department (MBC 16), King Faisal Specialist Hospital and Research Center, PO Box 3354, Riyadh 11211, Saudi Arabia. Fax. (966-1) 442-7482.

Summary

A rare association of ‘absent pulmonary valve’ syndrome, midmuscular ventricular septal defect and aneurysmatic dilation of the ascending aorta without pathology of the aortic valve is described in a 10-month-old infant. The diagnosis was established by echocardiography and angiography.

Type
Brief Reports
Copyright
Copyright © Cambridge University Press 1994

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