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A very unusual combination of straddling and overriding of the tricuspid valve associated with clefting of the mitral valve

Published online by Cambridge University Press:  13 July 2005

Liane Eberhardt ,
Philippe Chetaille  and
Bernard Kreitmann
Liane Eberhardt
Affiliation:
Department of Cardiology, Pediatric Cardiology Unit, Hôpital d'Enfants de la Timone, Marseille, France
Philippe Chetaille
Affiliation:
Department of Cardiology, Pediatric Cardiology Unit, Hôpital d'Enfants de la Timone, Marseille, France
Bernard Kreitmann
Affiliation:
Pediatric Thoracic and Cardiovascular Surgery, Hôpital d'Enfants de la Timone, Marseille, France
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Abstract

We describe a patient in whom we found dual orifices in a straddling and overriding tricuspid valve, with two normally sized ventricles and a cleft in the mitral valve. The patient underwent successful surgical repair. We discuss the concept of “double-orifice right atrium”, as well as the need to differentiate the isolated cleft of the morphologically mitral valve from the zone of apposition between the left ventricular components of the bridging leaflets seen in the setting of atrioventricular septal defect with common atrioventricular junction. We emphasise the unusual association of these abnormalities of the right and left atrioventricular valves in patients with separate atrioventricular junctions.

Keywords

Double-outlet right atriummitral insufficiencycongenital heart diseaseendocardial cushionssurgical repair
Type
Brief Report
Information
Cardiology in the Young , Volume 15 , Issue 4 , August 2005 , pp. 422 - 424
Copyright
© 2005 Cambridge University Press

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