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Unguarded tricuspid orifice with Uhl's malformation

Published online by Cambridge University Press:  19 August 2008

Brojendra Agarwala ,
J. Deane Waldman  and
Michele Carbone
Brojendra Agarwala*
Affiliation:
From the Sections of Pediatric Cardiology, Cardiovascular Surgery and Anatomic Pathology, and the Congenital Heart Registry, University of Chicago, Chicago
J. Deane Waldman
Affiliation:
From the Sections of Pediatric Cardiology, Cardiovascular Surgery and Anatomic Pathology, and the Congenital Heart Registry, University of Chicago, Chicago
Michele Carbone
Affiliation:
From the Sections of Pediatric Cardiology, Cardiovascular Surgery and Anatomic Pathology, and the Congenital Heart Registry, University of Chicago, Chicago
*
Dr. Brojendra Agarwala, Pediatric Cardiology, University of Chicago, 5841 South Maryland Avenue, Chicago, IL 60637, USA. Tel. 312-702-6172; Fax. 312-702-2319.
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Summary

A case is reported where unguarding of the tricuspid orifice was associated with Uhl's malformation. Echocardiographic features of the condition permitted the diagnosis during life. A therapeutic plan is proposed which involves surgical closure of the unguarded tricuspid orifice.

Keywords

Congenital heart surgeryFontan procedureEbstein's anomaly
Type
Brief Reports
Information
Cardiology in the Young , Volume 6 , Issue 2 , April 1996 , pp. 177 - 180
Copyright
Copyright © Cambridge University Press 1996

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References

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