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Total anomalous pulmonary venous connection mimicking hypoplastic left heart syndrome

Published online by Cambridge University Press:  04 May 2021

Ryohei Matsuoka
Affiliation:
Department of Pediatrics, Japan Community Healthcare Organization Kyusyu Hospital, Kitakyusyu, Japan
Jun Muneuchi*
Affiliation:
Department of Pediatrics, Japan Community Healthcare Organization Kyusyu Hospital, Kitakyusyu, Japan
Yoshie Ochiai
Affiliation:
Department of Cardiovascular Surgery, Japan Community Healthcare Organization Kyusyu Hospital, Kitakyusyu, Japan
*
Author for correspondence: J. Muneuchi, MD, Department of Pediatrics, Japan Community Healthcare Organization Kyusyu Hospital, 1-8-1, Kishinoura, Yahatanishi-ku, Kitakyushu, Fukuoka 806-8501, Japan. Tel: +81-93-641-5111. E-mail: [email protected]

Abstract

A newborn with supracardiac total anomalous pulmonary venous connection vein presented the small left ventricle with z score of −7.5, retrograde blood supply in the transverse arch, and the dutcus-dependent systemic circulation. The patient underwent the repair of the anomalous pulmonary vein and bilateral pulmonary arterial banding soon after the birth and then transcatheter pulmonary arterial debanding at the age of 10 months because of an appropriate growth of the left ventricle.

Type
Brief Report
Copyright
© The Author(s), 2021. Published by Cambridge University Press

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References

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