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Spontaneous improvement of severe right ventricular dysfunction in the setting of hypoplasia of the left heart

Published online by Cambridge University Press:  14 April 2005

Vivek Muthurangu ,
John M. Simpson  and
Reza S. Razavi
Vivek Muthurangu
Affiliation:
Cardiac MR Research Group, Division of Imaging Sciences, King's College, London, United Kingdom
John M. Simpson
Affiliation:
Department of Congenital Heart Disease, Guy's Hospital, London, United Kingdom
Reza S. Razavi
Affiliation:
Cardiac MR Research Group, Division of Imaging Sciences, King's College, London, United Kingdom Department of Congenital Heart Disease, Guy's Hospital, London, United Kingdom
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Abstract

Right ventricular dysfunction is known to occur after the first stage of the Norwood sequence for treatment of patients with hypoplasia of the left heart. In a subset of patients, such ventricular dysfunction occurs without a specific anatomical cause. We describe two such cases with severe right ventricular dysfunction. In both cases, magnetic resonance imaging was used accurately to measure ventricular function and assess the arterial trunks. In both cases, cardiac transplantation was considered, but right ventricular function improved without invasive management. Transient right ventricular dysfunction in these cases may be due to the reduced ability of the right ventricle to adapt to the systemic vasculature. The improvement in ventricular function in these two cases may be due to delayed adaptation.

Keywords

Hypoplastic left heartmagnetic resonance imagingright ventricular function
Type
Brief Report
Information
Cardiology in the Young , Volume 15 , Issue 1 , January 2005 , pp. 75 - 78
Copyright
2005 Cambridge University Press

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