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Right ventricular noncompaction in a neonate with complex congenital heart disease

Published online by Cambridge University Press:  13 July 2005

Dursun Alehan  and
Omer Faruk Dogan
Dursun Alehan
Affiliation:
Division of Pediatric Cardiology, Hacettepe University Faculty of Medicine, Sihhiye, Ankara, Turkey
Omer Faruk Dogan
Affiliation:
Department of Cardiovascular Surgery, Hacettepe University Faculty of Medicine, Sihhiye, Ankara, Turkey
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Abstract

Ventricular noncompaction is a rare unclassified cardiomyopathy occurring because of arrest of the normal intrauterine compaction of the loose luminal component of the ventricular myocardium. There is limited data regarding its diagnosis and outcome in children. It is recognised, however, that right ventricular involvement is extremely rare. We report a case in which only the right ventricular myocardium was noncompacted, a situation which led to heart failure soon after birth.

Keywords

Cardiomyopathyechocardiographycardiac failure
Type
Brief Report
Information
Cardiology in the Young , Volume 15 , Issue 4 , August 2005 , pp. 434 - 436
Copyright
© 2005 Cambridge University Press

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