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Resection of ventricular rhabdomyomas in infants presenting with cardiac failure

Published online by Cambridge University Press:  01 December 2008

Narendra R. Dereddy ,
Suvro S. Sett  and
Usha Krishnan
Narendra R. Dereddy
Affiliation:
Department of Pediatrics, Maria Fareri Children’s Hospital, Westchester Medical Center, Valhalla, New York, United States of America
Suvro S. Sett
Affiliation:
Department of Cardiovascular Surgery, Maria Fareri Children’s Hospital, Westchester Medical Center, Valhalla, New York, United States of America
Usha Krishnan*
Affiliation:
Department of Pediatric Cardiology, Maria Fareri Children’s Hospital, Westchester Medical Center, Valhalla, New York, United States of America
*
Correspondence to: Usha Krishnan, MD, Division of Pediatric Cardiology, 618, Munger Pavilion, New York Medical College, Valhalla, NY 10595, USA. Tel: +1 (914) 493 8372; Fax: +1 (914) 594 4513; E-mail: [email protected]
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Abstract

Rhabdomyomas are the most common cardiac tumours in children. They sometimes cause significant obstruction of the ventricular out flow tracts. We report a series of 3 neonates diagnosed antenatally with multiple rhabdomyomas, who developed significant obstruction of the ventricular outflow tracts following birth. They underwent surgical resection in the neonatal period with good outcome. Antenatal diagnosis of obstructive cardiac tumours allows for planning for appropriate early intervention.

Keywords

Cardiac tumourstuberous sclerosisventricular outflow tract obstruction
Type
Brief Report
Information
Cardiology in the Young , Volume 18 , Issue 6 , December 2008 , pp. 635 - 637
Copyright
Copyright © Cambridge University Press 2008

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References

1.McAllister, HA Jr. Primary tumours of the heart and pericardium. Pathol Annals 1979; 14: 325–355.Google Scholar
2.Holley, DG, Martin, GR, Brenner, JI, et al. Diagnosis and management of fetal cardiac tumours, a multicenter experience and review of published reports. J Am Coll Cardiol 1995; 26: 516–520.CrossRefGoogle ScholarPubMed
3.Beghttti, M, Gow, RM, Haney, I, Mawson, J, Williams, WG, Freedom, RM. Pediatric primary benign cardiac tumours: a 15 years review. Am Heart J 1997; 134: 1107–1114.Google Scholar
4.Fenoglio, JJ, Mc Allister, HA, Ferrans, VJ. Cardiac rhabdomyoma: A clinicopathologic and electron microscopic study. Am J Cardiol 1976; 38: 241–251.Google Scholar
5.Nir, A, Tajik, J, Freeman, WK, et al. Tuberous sclerosis and rhabdomyoma. Am J Cardiol 1995; 76: 419–421.CrossRefGoogle ScholarPubMed
6.Smith, HC, Watson, GH, Patel, RG, Super, M. Cardiac rhabdomyomata in tuberous sclerosis: their course and diagnostic value. Arch Dis Child 1989; 64: 196–200.CrossRefGoogle ScholarPubMed
7.Muhler, EG, Kienast, W, Turniski-Harder, V, Von Bernuth, G. Arrhythmias in infants and children with primary cardiac tumours. Eur Heart J 1994; 15: 915–921.Google Scholar
8.Ibrahim, CP, Thakker, P, Miller, PA, Barron, D. Cardiac rhabdomyoma presenting as left ventricular outflow tract obstruction in a neonate. Interact Cardiovasc Thorac Surg 2003; 2: 572–574.Google Scholar
9.Black, MD, Kadletz, M, Smallhorn, JF, Freedom, RM. Cardiac rhabdomyomas and obstructive left heart disease: histologically but not functionally benign. Ann Thorac Surg 1998; 65: 1388–1390.Google Scholar