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Progressive fetal atrioventricular block in heterotaxy syndrome

Published online by Cambridge University Press:  18 June 2007

Sethuraman Swaminathan  and
Anitha Parthiban
Sethuraman Swaminathan*
Affiliation:
Division of Cardiology, Department of Pediatrics, University of Miami-Miller School of Medicine, Miami, Florida, Unites States of America
Anitha Parthiban
Affiliation:
Division of Cardiology, Department of Pediatrics, University of Miami-Miller School of Medicine, Miami, Florida, Unites States of America
*
Correspondence to: Sethuraman Swaminathan, MD, Department of Pediatrics (Cardiology), University of Miami Miller School of Medicine, PO Box 016960 (R-76), Miami, Florida 33101, USA. Tel: +(305) 585 6683; Fax: +(305) 324 6012; E-mail: [email protected]
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Abstract

We report a fetus with left isomerism, in whom the atrioventricular block progressed from low grade second degree to complete block and fetal hydrops. While it is known that there is a high incidence of heart block in the fetus with left isomerism, as far as we are aware, ours is the first report of Wenckebach type block documented in the fetus by Doppler echocardiography, and demonstration of the progression of heart block during fetus life in the setting of left isomerism.

Keywords

Wenckebach phenomenonfetal echocardiogramleft isomerism
Type
Brief Report
Information
Cardiology in the Young , Volume 17 , Issue 4 , August 2007 , pp. 432 - 434
Copyright
Copyright © Cambridge University Press 2007

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