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A most peculiar coronary circulation in a patient with pulmonary atresia and intact ventricular septum

Published online by Cambridge University Press:  19 August 2008

Robert M. Freedom ,
Shi-Joon Yoo  and
Alexander Javois
Robert M. Freedom*
Affiliation:
Division of Cardiology, Department of Pediatrics, Department of Medical Imaging, the University of Toronto, Faculty of Medicine, Toronto, Canada;
Shi-Joon Yoo
Affiliation:
Division of Cardiology and Department of Pediatrics, the Hospital for Sick Children, Toronto, Canada
Alexander Javois
Affiliation:
The Heart Institute for Children, Hope Children's Hospital, Oak Lawn, Ill., USA
*
Robert M. Freedom, MD, The Hospital for Sick Children, 555 University Avenue, Room 1503C, Toronto, Canada M5G 1X8; Tel: 416–8136132; Fax: 416–8137547
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Abstract

A patient with pulmonary atresia and intact ventricular septum was found to have a right ventricular-dependent coronary circulation. In this infant both coronary arteries lacked their normal proximal connection with the aorta, perhaps the most egregious form of this prejudicial coronary circulation. Even more interesting was a direct collateral vessel originating from the descending thoracic aorta and connecting with the coronary circulation. This patient has undergone bilateral modified Blalock-Taussig shunts, and left ventricular function seems preserved.

Keywords

pulmonary atresia and intact ventricular septumcollateral coronary artery circulationabsent aorto-coronary artery proximal connectionsright ventricular-dependent coronary circulationFontan operation
Type
Brief Reports
Information
Cardiology in the Young , Volume 10 , Issue 1 , January 2000 , pp. 60 - 63
Copyright
Copyright © Cambridge University Press 2000

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