Hostname: page-component-586b7cd67f-dlnhk Total loading time: 0 Render date: 2024-11-23T09:13:34.177Z Has data issue: false hasContentIssue false
  • English
  • Français

Hypoplasia of the left heart with discordant ventriculoarterial connections

Published online by Cambridge University Press:  18 November 2005

Thomas Borth-Bruhns ,
Gerhard Ziemer  and
Michael Hofbeck
Thomas Borth-Bruhns
Affiliation:
Pediatric Cardiology, University Children's Hospital, Tübingen, Germany
Gerhard Ziemer
Affiliation:
Cardiothoracic Surgery, University Hospital, Tübingen, Germany
Michael Hofbeck
Affiliation:
Pediatric Cardiology, University Children's Hospital, Tübingen, Germany
Get access Rights & Permissions [Opens in a new window]

Abstract

We report the rare combination of a severely hypoplastic left ventricle and discordant ventriculoarterial connections, with associated subpulmonary obstruction of the left ventricular outflow tract. The long tortuous arterial duct originated at an acute angle from the aorta, suggesting that the subpulmonary obstruction developed early in fetal life. Residual flow via the hypoplastic left ventricle to the pulmonary circulation after insertion of an aortopulmonary shunt resulted in haemodynamic deterioration, which was instantly reversed by closing the pulmonary trunk.

Keywords

Hypoplastic left heart syndrometransposition of the great arteriesfunctionally univentricular heart
Type
Brief Report
Information
Cardiology in the Young , Volume 15 , Issue 6 , December 2005 , pp. 650 - 653
Copyright
© 2005 Cambridge University Press

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

Leitner G, Hammerer I. Agenesis of the ductus arteriosus Botalli and premature closure of the foramen ovale, in combination with mitral valve atresia, hypoplastic left ventricle, transposition of the great arteries, and pulmonary valve atresia. Pathol Res Pract 1980; 170: 410–419.Google Scholar
Lang D, Hofstetter R, Kupferschmid C. Hypoplastic left heart with complete transposition of the great arteries. Br Heart J 1985; 53: 650–653.Google Scholar
Ho SY, Angelini A, Russell G. Pulmonary atresia with hypoplastic left ventricle. Int J Cardiol 1987; 15: 349–352.Google Scholar
Oberhoffer R, Lang D, Schmaltz AA, Kupferschmid C. Hypoplastic left heart with transposition of the great arteries. Z Kardiol 1988; 77: 64–68.Google Scholar
Shiono N, Takanashi Y, Yoshihara K, et al. Successful surgical treatment of total cavopulmonary connection on a 4-year-old boy with complete transposition of the great arteries and hypoplastic left ventricle. Nippon Kyobu Geka Gakkai Zasshi 1995; 43: 884–888.Google Scholar
Nakata S, Imai Y, Takanashi Y, et al. A new method for the quantitative standardization of cross-sectional areas of the pulmonary arteries in congenital heart diseases with decreased pulmonary blood flow. J Thorac Cardiovasc Surg 1984; 88: 610–619.Google Scholar
Abrams S, Walsh K. Arterial duct morphology with reference to angioplasty and stenting. Int J Cardiol 1993; 40: 27–33.Google Scholar
Santos MA, Moll JN, Drumond C, Araujo WB, Romao N, Reis NB. Development of the ductus arteriosus in right ventricular out-flow tract obstruction. Circulation 1980; 62: 818–822.Google Scholar
Mildner RJ, Kiraly L, Sreeram N. Pulmonary atresia, “intact ventricular septum”, and aortopulmonary collateral arteries. Heart 1997; 77: 173–175.Google Scholar