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Genetic dilated cardiomyopathy with inflammation in an infant that responded to immunosuppressive therapy evaluated using cardiovascular magnetic resonance

Published online by Cambridge University Press:  12 April 2024

Hiromitsu Shirozu Open the ORCID record for Hiromitsu Shirozu [Opens in a new window] ,
Yuichi Ishikawa Open the ORCID record for Yuichi Ishikawa [Opens in a new window]  and
Nobuhiko Kan
Hiromitsu Shirozu*
Affiliation:
Department of Pediatric Cardiology, Fukuoka Children’s Hospital, Fukuoka, Japan
Yuichi Ishikawa
Affiliation:
Department of Pediatric Cardiology, Fukuoka Children’s Hospital, Fukuoka, Japan
Nobuhiko Kan
Affiliation:
Department of Pediatric Cardiology, Fukuoka Children’s Hospital, Fukuoka, Japan
*
Corresponding author: Hiromitsu Shirozu; Email: [email protected]
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Abstract

Cardiovascular magnetic resonance T1 and T2 mapping reflects inflammation, fibrosis, and myocardial oedema. However, its application in infants remains uncertain. Herein, we report a three-month-old boy with dilated cardiomyopathy successfully treated with steroids. Cardiovascular magnetic resonance was useful for diagnosis based on the elevated native T1, T2, and extracellular volume and evaluation of response to immunosuppressive therapy in infantile inflammatory dilated cardiomyopathy.

Keywords

dilated cardiomyopathycardiovascular magnetic resonanceT1T2 mapping
Type
Brief Report
Information
Cardiology in the Young , Volume 34 , Issue 6 , June 2024 , pp. 1352 - 1354
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Copyright
© The Author(s), 2024. Published by Cambridge University Press

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References

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