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Double orifice left atrioventricular valve—diagnosis and management of an unexpected lesion

Published online by Cambridge University Press:  19 August 2008

David B. Brieger ,
Cameron Ward ,
Stephen G. Cooper ,
Graham R. Nunn ,
Timothy B. Cartmill  and
Gary F. Sholler
David B. Brieger
Affiliation:
From The Adolph Basser Institute of Cardiology, Royal Alexandra Hospital for Children, Sydney
Cameron Ward
Affiliation:
From The Adolph Basser Institute of Cardiology, Royal Alexandra Hospital for Children, Sydney
Stephen G. Cooper
Affiliation:
From The Adolph Basser Institute of Cardiology, Royal Alexandra Hospital for Children, Sydney
Graham R. Nunn
Affiliation:
From The Adolph Basser Institute of Cardiology, Royal Alexandra Hospital for Children, Sydney
Timothy B. Cartmill
Affiliation:
From The Adolph Basser Institute of Cardiology, Royal Alexandra Hospital for Children, Sydney
Gary F. Sholler*
Affiliation:
From The Adolph Basser Institute of Cardiology, Royal Alexandra Hospital for Children, Sydney
*
Dr. G. Sholler, The Adolph Basser Institute of Cardiology, Royal Alexandra Hospital for Children, PO Box 34, Camperdown, Sydney 2050, Australia.
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Abstract

Double orifice left atrioventricular valve is an uncommon condition. This paper describes 10 consecutive patients with the anomaly encountered over 20 months. Diagnosis was assisted by cross-sectional echocardiography and supplementary color Doppler, often requiring non-standard views and a high index of suspicion. There were three anatomical variants—those in which the orifices were equal in size (three of 10 patients), those in which they were unequal and associated with an atrioventricular septal defect (four of 10 patients), and those in which they were unequal in the absence of an atrioventricular septal defect (three of 10 patients). The unequal orifice in both anatomical situations was frequently complicated by valvar regurgitation (six of seven patients). Conservative repair was possible in three of the four patients requiring surgery to the left atrioventricular valve. This condition should be thought of more often in the differential diagnosis of left atrioventricular regurgitation in childhood.

Keywords

Double orifice left atrioventricular valve and echocardiographydouble orifice left atrioventricular valve and valvar regurgitationmitral valve
Type
Original Manuscripts
Information
Cardiology in the Young , Volume 5 , Issue 3 , July 1995 , pp. 267 - 271
Copyright
Copyright © Cambridge University Press 1995

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