Hostname: page-component-586b7cd67f-rcrh6 Total loading time: 0 Render date: 2024-11-23T04:44:58.805Z Has data issue: false hasContentIssue false
  • English
  • Français

Diagnosis and management of congenital right pulmonary venous atresia

Published online by Cambridge University Press:  23 October 2009

I. Ricardo Argueta-Morales ,
Ruchira Garg  and
William M. DeCampli
I. Ricardo Argueta-Morales
Affiliation:
Congenital Heart Institute at Arnold Palmer Hospital and Miami Children’s Hospital, Arnold Palmer Hospital for Children, Orlando, Florida
Ruchira Garg
Affiliation:
Congenital Heart Institute at Arnold Palmer Hospital and Miami Children’s Hospital, Miami Children’s Hospital, Miami, Florida
William M. DeCampli*
Affiliation:
Congenital Heart Institute at Arnold Palmer Hospital and Miami Children’s Hospital, Arnold Palmer Hospital for Children, Orlando, Florida
*
Correspondence to: William M. DeCampli, MD, PhD, Congenital Heart Institute, Arnold Palmer Hospital for Children, 50 West Sturtevant Street, Orlando, Florida, USA 32806. Phone: 407-649-6907; Fax: 321-841-4260; E-mail: [email protected]
Get access Rights & Permissions [Opens in a new window]

Abstract

Congenital unilateral pulmonary venous atresia is a rare anatomical defect. Patients present with pulmonary symptoms, and diagnosis may be ellusive. Pulmonary arterial wedge angiography is the gold standard with which to achieve diagnosis, and surgical intervention is often required for symptomatic patients.

Keywords

Heart defectsunilateral pulmonary venous atresiacongenital malformations
Type
Brief Reports
Information
Cardiology in the Young , Volume 19 , Issue 6 , December 2009 , pp. 648 - 651
Copyright
Copyright © Cambridge University Press 2009

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1.Artero, I, Serrano, F, Padín, MI, Serrano, F. Atresia congenita unilateral de las venas pulmonares: hallazgos radiologicos [Congenital unilateral pulmonary vein atresia: imaging findings]. Radiología 2008; 50: 82–85.CrossRefGoogle Scholar
2.Heyneman, LE, Nolan, RL, Harrison, JK, McAdams, HP. Congenital unilateral pulmonary vein atresia: radiologic findings in three adult patients. AJR 2001; 177: 681–685.CrossRefGoogle ScholarPubMed
3.Pourmoghadam, KK, Moore, JW, Khan, M, et al. Congenital unilateral pulmonary venous atresia: definitive diagnosis and treatment. Pediatr Cardiol 2003; 24: 73–79.CrossRefGoogle ScholarPubMed
4.Masui, T, Seelos, KC, Kersting-Sommerhoff, BA, Higgins, CB. Abnormalities of the pulmonary veins: evaluation with MR imaging and comparison with cardiac angiography and echocardiography. Radiology 1991; 181: 645–649.Google Scholar
5.Roman, KS, Kellemberger, CJ, Macgowan, CK, et al. How is pulmonary arterial blood flow affected by pulmonary venous obstruction in children? A phase-contrast magnetic resonance study. Peditr Radiol 2005; 35: 580–586.CrossRefGoogle Scholar
6.Grosse-Wortmann, L, Hamilton, R, Yoo, SJ. Massive systemic-to-pulmonary collateral arteries in the setting of a cavopulmonary venous stenosis. Cardiol Young 2007; 17: 548–550.CrossRefGoogle ScholarPubMed
7.Sutton, NJ, Peng, L, Lock, JE, et al. Effect of pulmonary artery angioplasty on exercise function after repair of tetralogy of Fallot. Am Heart J 2008; 155: 182–186.CrossRefGoogle ScholarPubMed