Hostname: page-component-586b7cd67f-rdxmf Total loading time: 0 Render date: 2024-11-23T01:41:58.213Z Has data issue: false hasContentIssue false
  • English
  • Français

Conversion of the modified Fontan operation to total cavopulmonary connection: a treatment for protein-losing enteropathy

Published online by Cambridge University Press:  19 August 2008

Gerd Stafanger ,
Gösta Pettersson  and
Joes Ramsøe Jacobsen
Gerd Stafanger*
Affiliation:
Department of Paediatrics and Cardiothoracic Surgery, Rigshospital, Copenhagen, Denmark
Gösta Pettersson
Affiliation:
Department of Paediatrics and Cardiothoracic Surgery, Rigshospital, Copenhagen, Denmark
Joes Ramsøe Jacobsen
Affiliation:
Department of Paediatrics and Cardiothoracic Surgery, Rigshospital, Copenhagen, Denmark
*
Gerd Stafanger, Department of Paediatrics GGK 5004, Rigshospital, Blegdamsvej 9, DK 2100 Copenhagen Ø, Denmark. Tel: 35453825, Fax: 42307386
Get access Rights & Permissions [Opens in a new window]

Abstract

We describe a patient with tricuspid atresia who, after a Fontan operation three years earlier, presented with severe protein-losing enteropathy. After conversion to a cavopulmonary connection, the symptoms regressed and substitution with albumin and immunoglobulin was no longer required.

Keywords

Tricuspid atresiaFontan operationprotein-losing enteropathy
Type
Brief Reports
Information
Cardiology in the Young , Volume 7 , Issue 3 , July 1997 , pp. 344 - 346
Copyright
Copyright © Cambridge University Press 1997

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1.Fontan, F, Baudet, E. Surgical repair of tricuspid atresia. Thorax 1971; 26: 240–248.CrossRefGoogle ScholarPubMed
2.Driscoll, DJ, Offord, KP, Feldt, RH, Schaff, HV, Puga, FJ, Danielsen, GK. Five- to Fifteen-Year Follow-up After Fontan Operation. Circulation 1992; 85: 469–496.CrossRefGoogle ScholarPubMed
3.Davis, CA, Driscoll, DJ, Perrault, J, Greenwood, DH, Schaff, HV, Puga, FJ, Danielson, GK, Feldt, RH. Enteric Protein Loss After the Fontan Operation. Mayo Clin Proc 1994; 69: 112–114.CrossRefGoogle ScholarPubMed
4.Hess, J, Kruizinga, K, Bijlevel, DMA, Hardjowijono, R, Eygelaar, R. J Thorac Cardiovasc Surg 1984; 88: 606–609.CrossRefGoogle Scholar
5.Mair, DD, Puga, FJ, Danielsen, GK. Late functional status of survivors of the Fontan procedure performed during the 1970s. Circulation 1992; 86 (suppl II):II–106–II–109.Google ScholarPubMed
6.de Leval, MR, Kilner, P, Gewillig, M, Bull, C. Total cavopulmonary connection: A logical alternative to atropulmonary connection for complex Fontan operations. J Thorac Cardiovasc Surg 1988; 96: 682–95.CrossRefGoogle ScholarPubMed
7.Mertens, L, Dumoulin, M, Gewillig, M. Effect of percutaneous fenestration of the atrial septum on protein-losing enteropathy after the Fontan operation. Br Heart J 1994; 72: 591–592.CrossRefGoogle ScholarPubMed