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Congenital quadricuspid aortic valve in children

Published online by Cambridge University Press:  01 June 2008

Alfredo Di Pino ,
Placido Gitto ,
Antonio Silvia  and
Innocenzo Bianca
Alfredo Di Pino*
Affiliation:
Paediatric Cardiology, San Vincenzo Hospital, Taormina, Messina, Italia
Placido Gitto
Affiliation:
Paediatric Cardiology, San Vincenzo Hospital, Taormina, Messina, Italia
Antonio Silvia
Affiliation:
Paediatric Cardiology, San Vincenzo Hospital, Taormina, Messina, Italia
Innocenzo Bianca
Affiliation:
Paediatric Cardiology, San Vincenzo Hospital, Taormina, Messina, Italia
*
Correspondence to: Alfredo Di Pino, Unità Operativa di Cardiologia Pediatrica, Ospedale S. Vincenzo Contrada Sirina, 98039 Taormina Messina. Tel: 0942579850; Fax: 094252215; E-mail: [email protected]
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Abstract

Quadricuspid aortic valves are rare congenital anomalies, usually diagnosed in adult patients affected by severe aortic regurgitation. We have now encountered three such valves in children undergoing transthoracic echocardiography. All children were asymptomatic. The first child possessed a valve with two larger leaflets, and smaller leaflets of equal size. In the second child, 3 leaflets were of equal size, with 1 small accessory leaflet. The third child had a valve with four leaflets of approximately equal size. In one child, the aortic valve was functioning normally, and came to attention because of mitral valvar prolapse causing mild regurgitation. In the remaining two children, central mild aortic regurgitation was detected using colour flow analysis, and associated dilation of the aortic root was revealed by measurements of the cross-sectional images.

Keywords

Arterial valveregurgitationaortic root
Type
Original Article
Information
Cardiology in the Young , Volume 18 , Issue 3 , June 2008 , pp. 324 - 327
Copyright
Copyright © Cambridge University Press 2008

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