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Cardiac anomalies in the setting of the Abernethy malformation of the portal vein

Published online by Cambridge University Press:  22 December 2006

Christopher Ratnasamy ,
Amethyst Kurbegov  and
Sethuraman Swaminathan
Christopher Ratnasamy
Affiliation:
Division of Pediatric Cardiology, University of Miami – Miller School of Medicine, Miami, Florida, United States of America
Amethyst Kurbegov
Affiliation:
Division of Pediatric Gastroenterology, University of Miami – Miller School of Medicine, Miami, Florida, United States of America
Sethuraman Swaminathan
Affiliation:
Division of Pediatric Cardiology, University of Miami – Miller School of Medicine, Miami, Florida, United States of America
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Abstract

We describe a child with tricuspid atresia associated with a porto-systemic shunt and complete absence of the portal vein, the latter known as the Abernethy malformation. As far as we are aware, this association has not previously been reported. We review the various cardiac defects that have been reported in children with the Abernethy malformation, emphasizing the interesting clinical presentations of this rare malformation of the portal venous system.

Keywords

Tricuspid atresiaporto-systemic shuntencephalopathy
Type
Brief Report
Information
Cardiology in the Young , Volume 17 , Issue 2 , April 2007 , pp. 212 - 214
Copyright
© 2007 Cambridge University Press

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