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Atrioventricular septal defect with an imperforate right-sided component of the common atrioventricular valve: anatomic and embryologic considerations

Published online by Cambridge University Press:  10 July 2013

Lazaro E. Hernandez ,
Lazaros K. Kochilas  and
Robert H. Anderson
Lazaro E. Hernandez*
Affiliation:
Department of Pediatrics, Amplatz Children's Hospital, University of Minnesota, Minneapolis, Minnesota, United States of America
Lazaros K. Kochilas
Affiliation:
Department of Pediatrics, Amplatz Children's Hospital, University of Minnesota, Minneapolis, Minnesota, United States of America
Robert H. Anderson
Affiliation:
Department of Pediatrics, Institute of Medical Genetics, Newcastle University, Newcastle-upon-Tyne, United Kingdom
*
Correspondence to: L. E. Hernandez, MD, 2540 Riverside Ave, East 5th floor, Minneapolis, Minnesota, United States of America. Tel: 612-626-2755; Fax: 612-626-2467; E-mail: email: [email protected]
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Abstract

We describe an atypical case of an atrioventricular septal defect with a common atrioventricular junction in which the right-sided component of the common atrioventricular valve was imperforate, producing tricuspid atresia with a severely hypoplastic right ventricle and an ostium primum defect. We discuss the implications of the anatomic findings with regard to concepts of cardiac development, drawing a comparison with similar cases previously reported.

Keywords

Imperforate atrioventricular valveostium primumhypoplastic right ventricle
Type
Brief Reports
Information
Cardiology in the Young , Volume 24 , Issue 3 , June 2014 , pp. 540 - 542
Copyright
Copyright © Cambridge University Press 2013 

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References

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