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An extremely rare association of coarctation of aorta with double chambered right ventricle: double-trouble causing bi-ventricular failure in a child

Published online by Cambridge University Press:  05 August 2021

Balaji Arvind
Affiliation:
Department of Cardiology, All India Institute of Medical Sciences, New Delhi, India
Sivasubramanian Ramakrishnan*
Affiliation:
Department of Cardiology, All India Institute of Medical Sciences, New Delhi, India
Velayoudam Devagourou
Affiliation:
Department of Cardiothoracic and Vascular Surgery, All India Institute of Medical Sciences, New Delhi, India
*
Author for correspondence: Dr Sivasubramanian Ramakrishnan DM, FACC, Professor of Cardiology, All India Institute of Medical Sciences, Room No. 29, 7th floor, Cardio-Thoracic Centre, New Delhi 110029, India. Tel: +91-011-26594861; Fax: +91-11-26588663. E-mail: [email protected]

Abstract

Double chambered right ventricle is a rare cardiac defect characterised by an obstructive hypertrophied muscle bundle in the right ventricle. The common associated lesions are ventricular septal defect followed by sub-aortic membrane. We report a child who had coarctation of aorta in association with double chambered right ventricle. This case is being reported for its rarity and challenges in management.

Type
Brief Report
Copyright
© The Author(s), 2021. Published by Cambridge University Press

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