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Acquired stenosis of normally connected pulmonary veins

Published online by Cambridge University Press:  20 April 2007

Shanta Chakrabarti ,
Ralph Mittal ,
James P Gnanapragasam  and
Robin P. Martin
Shanta Chakrabarti
Affiliation:
Bristol Congenital Heart Centre, Bristol Royal Hospital for Children, Bristol United Kingdom
Ralph Mittal
Affiliation:
Bristol Congenital Heart Centre, Bristol Royal Hospital for Children, Bristol United Kingdom
James P Gnanapragasam
Affiliation:
Department of Paediatric Cardiology, Southampton General Hospital, Southampton, United Kingdom
Robin P. Martin
Affiliation:
Bristol Congenital Heart Centre, Bristol Royal Hospital for Children, Bristol United Kingdom
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Abstract

Pulmonary venous stenosis has been a challenge to paediatric cardiologists and surgeons. In spite of significant improvements in the management and outcome of various congenital cardiac problems, the prognosis of this condition continues to be dismal. Acquired stenosis of the pulmonary veins has been described in the adult population, especially after radiofrequency ablation for atrial arrhythmias. The outcome of this condition has generally been described to be favourable in the long term. Acquisition of pulmonary venous stenosis in childhood has a very different outcome, and is not a very well recognised entity, with symptoms and signs which are non-specific. We present 7 infants who, when first assessed, had normal pulmonary veins, but who subsequently acquired stenoses of the veins, with very significant resultant morbidity and mortality.

Keywords

Pulmonary hypertensioncardiac surgerycutting balloon angioplastystentsechocardiography
Type
Original Article
Information
Cardiology in the Young , Volume 17 , Issue 3 , June 2007 , pp. 322 - 327
Copyright
© 2007 Cambridge University Press

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