Hostname: page-component-586b7cd67f-2plfb Total loading time: 0 Render date: 2024-11-26T07:22:50.624Z Has data issue: false hasContentIssue false
  • English
  • Français

Absent pulmonary valve in tricuspid atresia with left ventricular outflow tract obstruction and patent arterial duct

Published online by Cambridge University Press:  19 August 2008

Robert P. Lemke ,
Neils G. Giddins  and
Jonah N.K. Odim
Robert P. Lemke
Affiliation:
Variety Children's Heart Centre, Winnipeg, Manitoba, Canada
Neils G. Giddins
Affiliation:
Variety Children's Heart Centre, Winnipeg, Manitoba, Canada
Jonah N.K. Odim*
Affiliation:
Variety Children's Heart Centre, Winnipeg, Manitoba, Canada
*
Dr Jonah N.K. Odim, Director, Pediatric Cardiac Surgery, 685 William Avenue, Winnipeg, Manitoba, Canada, R3E 0Z2. Tel: (204) 787 2412, Fax: (204) 787 1419.
Get access Rights & Permissions [Opens in a new window]

Abstract

We describe a neonate with tricuspid atresia, absent pulmonary valve, right ventricular hypoplasia, small venrricular septal defect, left ventricular ourflow tract obstruction and a patent arterial duct. These finding were diagnosed by echocardiography and confirmed by cardiac catherterization and postmortem examination. This is a unique report of a functionally single ventricle variant of absent pulmonary valve syndrome and biventricular outlet obstuction.

Keywords

Absent pulmonary valve synfrometricuspid atresiapatent arterial duct
Type
Brief Report
Information
Cardiology in the Young , Volume 7 , Issue 1 , January 1997 , pp. 94 - 97
Copyright
Copyright © Cambridge University Press 1997

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1.Thanopoulos, BD, Fisher, EA, Hastreiter, AR. Large ductus arteriosus and intact ventricular septum associated with congenital absence of the pulmonary valve Br Heart J, 1986;55:602–604.Google Scholar
2.Alpert, BS, Moore, HV. “Absent” pulmonary valve with atrial septal defect and patient ductus arteriosus. Pediart Cardiol, 1985;6, 107–112.Google Scholar
3.Marin-Garcia, J, Roca, J, Blieden, LC, Lucas, RV, Edwards, JE. Congenital absence of the pulmonary valve associated with tricuspid acresia and intact ventrcular septum. Chest 1973;64:658–661.CrossRefGoogle Scholar
4.Freedom, RM, Patel, RG, Bloon, KR, Duckworth, JWA, Silver, MM, Dische, R, Rowe, RD.Congenital absence of the pulmonary valve associated with imperforate membrane type of tricuspid acresia, right ventricular tensor apparatus and intact ventricalar septim: a curious developmental complex. Europ J Cardiol, 1979;10:171–196.Google Scholar
5.Mori, KSatomi, G, Tohyama, K, Konishi, T, Momma, K, Nakamura, K, Takao, A. Membranous tricuspid atresia with right ventricular dysplasia and absent pumonary valve: echocardiographic findings in three sasses. J Cardiogr, 1986; 16:711–725.sGoogle Scholar
6.Ichinose, E, Hirata, K, Mikashima, T, Sakamoto, H, Toyoda, O, Yoshioka, F, Yokochi, K, Kato, H, Okada, R., Unusual cardiac hypertrophy in neonates with songestive heart failure:report of three caes. J Cardiogr. 1986;16:755–763.Google Scholar
7.Ettedgui, J, Sharland, G, Chita, S, Cook, A, Fagg, N, Lindsey, A. Absent pulmonary valve syndrome with ventricular septal efect: role of the arterial duct. Am J Card. 1990; 66: 233–234.Google Scholar
8.Momma, K, Ando, M, Takao, AFetal cardiac morphology of tetralogy of Fallot with absent pulmonary valve in the rat. Cirulation 1990; 82: 1343–1351.CrossRefGoogle ScholarPubMed
9.Johnason, MC, Strauss, AW, Dowton, SB, Spray, TL, Huddleston, CB, Wood, MK, Slaugh, RA, Watson, Ms.Deletion within chromosome 22 is common in patients with absent pulmonary valve syndrome. Am J Cardiol 1995;76:66–69.CrossRefGoogle Scholar
10.Horigome, H, Takano, T, Hirano, T, Kajima, T, Ohtani, s. Interstial deletion of the long arm of chromosome 6 associated with absent pulmonary valve in the rat. Circulation. 1990;82:608–611.Google Scholar