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The Abernethy malformation with inferior caval vein hypoplasia: a tailored technique for transcatheter closure and an insight into embryological perspective

Part of: Cardiac Morphology

Published online by Cambridge University Press:  06 July 2018

Ronak Sheth  and
Kothandam Sivakumar
Ronak Sheth
Affiliation:
Department of Pediatric Cardiology, Institute of Cardio Vascular Diseases, Madras Medical Mission, Chennai, India
Kothandam Sivakumar*
Affiliation:
Department of Pediatric Cardiology, Institute of Cardio Vascular Diseases, Madras Medical Mission, Chennai, India
*
Address for correspondence: Dr K. Sivakumar MD, DM, Head of Department of Pediatric Cardiology, Institute of Cardio Vascular Diseases, Madras Medical Mission, 4A, Dr J J Nagar, Mogappair, Chennai 600089, India. Tel: +91 9444449966; Fax +91 44 26565859; E-mail [email protected]
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Abstract

Abernethy malformations manifest as hepatopulmonary syndrome, pulmonary vasculopathy, or encephalopathy. A novel intervention in a child with portosystemic shunt and inferior caval vein hypoplasia led to complete normalisation of hypoxia and relief of obstruction in the inferior caval vein. Embryological explanations of venous anomalies may indicate that inferior caval vein anomalies are frequent but under-recognised in patients with Abernethy malformation.

Keywords

Abernethy malformationportosystemic shunthepatopulmonary syndromeinferior caval vein hypoplasiacovered stent
Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 9 , September 2018 , pp. 1169 - 1171
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Copyright
© Cambridge University Press 2018 

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Footnotes

Cite this article: Sheth R, Sivakumar K. (2018) The Abernethy malformation with inferior caval vein hypoplasia: a tailored technique for transcatheter closure and an insight into embryological perspective. Cardiology in the Young28: 1169–1171. doi: 10.1017/S1047951118000884

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