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Abnormal origin of the left pulmonary artery from the descending aorta and heterotaxy syndrome: an undescribed phenotypic association

Published online by Cambridge University Press:  04 June 2021

Anne Moreau de Bellaing*
Affiliation:
M3C-Necker, Hôpital Necker-Enfants Malades, AP-HP, Paris, France Department of Pediatric Cardiology, Université de Paris, Paris, France
Damien Bonnet
Affiliation:
M3C-Necker, Hôpital Necker-Enfants Malades, AP-HP, Paris, France Department of Pediatric Cardiology, Université de Paris, Paris, France
Lucile Houyel
Affiliation:
M3C-Necker, Hôpital Necker-Enfants Malades, AP-HP, Paris, France Department of Pediatric Cardiology, Université de Paris, Paris, France
*
Author for correspondence: Anne Moreau de Bellaing, MD, PhD, M3C-Necker, Necker-Enfants Malades, 149 rue de Sèvres, Paris 75015, France. Tel: +33(0)613471532; Fax: +33(0)144494340. E-mail: [email protected]

Abstract

Extensive screening in a newborn with prenatal suspicion of VACTERL syndrome identified an anomalous origin of the left pulmonary artery from the descending aorta with an arterial duct and left aortic arch, and normal intra-cardiac anatomy. Other anatomical anomalies suggested heterotaxy syndrome. At one-month-old, re-implantation of the 3.5 mm left pulmonary artery was performed by direct tension-low anastomosis. Post-operative course was complicated by severe left pulmonary atelectasis, and the patient died 20 days later.

Type
Brief Report
Copyright
© The Author(s), 2021. Published by Cambridge University Press

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