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Von Hippel-Lindau's Disease

Published online by Cambridge University Press:  18 September 2015

Robert G. Miller
Affiliation:
Departments of Neurology and Neurosurgery, University of California School of Medicine, San Francisco, California
Roger J. Porter*
Affiliation:
Departments of Neurology and Neurosurgery, University of California School of Medicine, San Francisco, California
Surl L. Nielsen
Affiliation:
Departments of Neurology and Neurosurgery, University of California School of Medicine, San Francisco, California
Hoshio Hosobuchi
Affiliation:
Departments of Neurology and Neurosurgery, University of California School of Medicine, San Francisco, California
*
Applied Neurologic Research Branch, National Institute of Neurological and Communicative Disorders and Stroke, National Institutes of Health, Bethesda, Maryland 20014
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Summary:

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A patient with Von Hippel-Lindau's disease was followed from the time of diagnosis to the time of his death 13 years later. He was asymptomatic when the diagnosis was made, although a hemangioblastoma of the medulla was found on angiography. The patient's course and autopsy are described and the features of this disease are reviewed.

Type
Research Article
Copyright
Copyright © Canadian Neurological Sciences Federation 1976

References

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