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Monomelic Atrophy

Published online by Cambridge University Press:  18 September 2015

J. Oryema ,
P. Ashby  and
S. Spiegel
J. Oryema
Affiliation:
EMG Department, Toronto Western Hospital, Toronto
P. Ashby*
Affiliation:
EMG Department, Toronto Western Hospital, Toronto
S. Spiegel
Affiliation:
EMG Department, Toronto Western Hospital, Toronto
*
Toronto Western Hospital, 399 Bathurst Street, Toronto, Ontario, Canada M5T 2S8
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Abstract:

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Weakness of distal muscles of one upper limb which progresses over 1 year and then appears to arrest (“monomelic amyotrophy”) has been reported mainly in Japan and India. We report 5 cases of a similar syndrome occurring in Canada. In our cases the wasting affected the forearm muscles of one upper limb (sparing brachioradialis and extensor carpi radialis). There was minimal wasting and electromyographic changes in the opposite upper limb. The CT myelogram showed unilateral wasting of the cervical cord.

Résumé:

RÉSUMÉ:

Une faiblesse musculaire distale au niveau d'un membre supérieur, qui évolue sur une période d'un an et qui semble ensuite arrêter de progresser (“amyotrophie monomélique”) a été rapportée surtout au Japon et aux Indes. Nous rapportons 5 cas d'un syndrome similaire survenus au Canada. Chez nos cas, l'atrophie atteignait les muscles de l'avant-bras d'un membre supérieur (épargnant le long supinateur et le radial). Il y avait peu d'atrophie et de changements électromyographiques dans le membre supérieur opposé. Le myélogramme par CT a montré une atrophie unilatérale de la moelle épinière cervicale.

Type
Original Articles
Information
Canadian Journal of Neurological Sciences , Volume 17 , Issue 2 , May 1990 , pp. 124 - 130
Copyright
Copyright © Canadian Neurological Sciences Federation 1990

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