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Electrocardiographic and Vectocardiographic Findings in Friedreich's Ataxia

Published online by Cambridge University Press:  18 September 2015

S. Malo ,
Y. Latour ,
M. Cote ,
G. Geoffroy ,
B. Lemieux  and
A. Barbeau
S. Malo
Affiliation:
Centre Hospitalier Universitaire de Sherbrooke; the Hôpital Hôtel-Dieu de Montréal; the Hôpital Ste-Justine de Montreal, and the Clinical Research Institute of Montreal
Y. Latour
Affiliation:
Centre Hospitalier Universitaire de Sherbrooke; the Hôpital Hôtel-Dieu de Montréal; the Hôpital Ste-Justine de Montreal, and the Clinical Research Institute of Montreal
M. Cote
Affiliation:
Centre Hospitalier Universitaire de Sherbrooke; the Hôpital Hôtel-Dieu de Montréal; the Hôpital Ste-Justine de Montreal, and the Clinical Research Institute of Montreal
G. Geoffroy
Affiliation:
Centre Hospitalier Universitaire de Sherbrooke; the Hôpital Hôtel-Dieu de Montréal; the Hôpital Ste-Justine de Montreal, and the Clinical Research Institute of Montreal
B. Lemieux
Affiliation:
Centre Hospitalier Universitaire de Sherbrooke; the Hôpital Hôtel-Dieu de Montréal; the Hôpital Ste-Justine de Montreal, and the Clinical Research Institute of Montreal
A. Barbeau*
Affiliation:
Centre Hospitalier Universitaire de Sherbrooke; the Hôpital Hôtel-Dieu de Montréal; the Hôpital Ste-Justine de Montreal, and the Clinical Research Institute of Montreal
*
Clinical Research Institute of Montreal, 110 Pine Avenue West, Montreal, Quebec, Canada H2W IR7
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Summary:

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Electrocardiographic and vectocardiographic changes are frequent in Friedreich's ataxia. In one of 35 patients both tests were normal. The vectocardiogram is more explicit in demonstrating the severity of the QRS changes with a right ventricular hypertrophy pattern present in 60% of cases. Serial examination and ECG tracings are recommended to monitor the cardiomyopathy in this progressive neurological disorder, in order to detect the onset of congestive heart failure, significant tachyarrythmias, or obstructive cardiomypathy.

Type
Quebec Cooperative Study of Friedreich's Ataxia
Information
Canadian Journal of Neurological Sciences , Volume 3 , Issue 4 , November 1976 , pp. 323 - 328
Copyright
Copyright © Canadian Neurological Sciences Federation 1976

References

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